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Siblings with Idiopathic Left Atrial Appendage Ostial Stenosis and Cor Triatriatum |
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| Authors: | Seigo Okada Ph.D. Yukiko Ishiguchi M.D. Yuji Moritoh M.D. Mayuko Shohi M.D. Naomi Nakagawa Ph.D. Kengo Okamoto M.D. Masahiro Kamada Ph.D. |
| Affiliation: | 1. Department of Pediatric Cardiology, Hiroshima City Hiroshima Citizens Hospital, Hiroshima, Japan;2. Department of Pediatrics, Yamaguchi University Graduate School of Medicine, Yamaguchi, Japan |
| Abstract: | Isolated left atrial appendage (LAA) ostial stenosis is a very rare entity found coincidentally in adults by transesophageal echocardiography. A 3‐month‐old healthy infant was suspected as having cor triatriatum. His brother had a history of surgical treatment of cor triatriatum. A cardiac catheterization revealed a narrowed ostium of the LAA and confirmed the echocardiographic diagnosis of isolated LAA ostial stenosis. This is the first pediatric case of idiopathic LAA ostial stenosis. The siblings called our attention to the differential diagnosis and the etiopathogenesis between LAA ostial stenosis and cor triatriatum. |
| Keywords: | congenital heart disease cor triatriatum left atrium left atrial appendage function ostial stenosis |