Recurrent retroperitoneal cystic lymphangioma

Retroperitoneal cystic lymphangioma is a rare congenital malformation. The majority of lymphangiomas are present at birth and nearly all present before the age of two years. We report a case of giant cystic retroperitoneal lymphangioma in a patient who first presented with symptoms at the age of 7, underwent surgery, and who then suffered a recurrent mass 11 years later.     

Intrapulmonary cystic lymphangioma in a 2-month-old infant.

Lymphangioma is an abnormal collection of lymphatics that are developmentally isolated from the normal lymphatic system. Lymphangioma rarely presents as a solitary pulmonary lesion. We report a rare case of intrapulmonary cystic lymphangioma involving the upper lobe of the right lung, which presented with dyspnea in a 2-month-old infant. High-resolution computed tomography (HRCT) of the chest demonstrated a well-circumscribed, multiseptate, cystic lesion in the upper lobe of the right lung, mimicking the feature of type I congenital cystic adenomatoid mal-formation. The tumor was removed by bilobectomy of the upper and middle lobes of the right lung, and its pathologic examination confirmed the diagnosis of an intra-pulmonary cystic lymphangioma.     

Mediastinal lymphangioma in adults: CT and MR imaging features

Adult mediastinal lymphangiomas are rare lesions the diagnosis of which is difficult based on imaging studies. A retrospective study of CT, MR, and pathologic findings of mediastinal lymphangioma was performed in order to correlate pathological and imaging findings. Nine cases of adult lymphangiomas were identified in the records of our institution over a 12-year period. The CT, MR, and pathologic findings were reviewed. Lesions were classified pathologically as unilocular, cavernous, and intermediate types. Pathologic examination identified six cases of unilocular lesion, two cases of cavernous type, and one intermediate type. The CT features (n = 9) included a smoothly marginated non-enhancing mass of water attenuation (n = 7), a non-enhancing mass of soft tissue attenuation (n = 1), and an enhancing multiseptated mass (n = 1). Lesions were located in the anterior mediastinum (n = 2), right paratracheal (n = 4), subcarinal (n = 1), aortopulmonic window (n = 1) areas, and below the left hilum extending into the posterior mediastinum (n = 1). The MR features (n = 3) were characterized by an enhancing multicystic and multiseptated appearance, evocative of a cavernous type in two cases. The CT appearance of mediastinal thoracic lymphangioma is variable depending on the pathologic type. The most common unilocular type is a non-enhancing thin-walled mass on CT. A less frequent cavernous type can be suggested based on a multiseptated and loculated mass on CT and/or MR examination. Received: 21 June 1999; Revised: 30 September 1999; Accepted: 23 February 2000     

Bleomycin sclerotherapy in lymphangiomas of the head and neck region: a prospective study

Intralesional sclerotherapy for lymphatic malformations (LMs) has become a modality of choice because of the high morbidity and recurrence rates with surgical excision. Traditionally, the macrocystic variant has shown good results with sclerotherapy. This prospective study was performed to evaluate the role of bleomycin sclerotherapy in the management of different radiological variants of LM. A total of 142 patients were included in this study. The lesions were classified as macrocystic, microcystic, or mixed LMs on the basis of ultrasonography. All patients were managed by intralesional injection of bleomycin and were recalled after 4 weeks for evaluation. Colour photographs of the patients were taken before the onset of treatment and at each monthly visit, and were utilized to assess the response. Following the second, third, and fourth doses, the response was better in patients with the macrocystic variant than in those with the other two variants. However, after the completion of six doses, 80.3% of patients with the macrocystic variant, 67.4% with the microcystic variant, and 71.4% with the mixed type had a complete response. There was no difference in the overall response between the three types (P = 0.28). Oedema, erythema, and local induration with fever were the most common adverse effects and were more common in younger children.     

Bilateral lymphangiomatous polyps of the palatine tonsils

Lymphangiomatous polyps of the tonsils are rare with less than 30 cases reported in the literature. All have been unilateral. We report a case of a child with bilateral lymphangiomatous polyps of the palatine tonsils that was suspected on preoperative examination as opposed to an incidental postoperative histologic finding. These findings were also correlated with a further imaging study to establish this entity as a localized rather than a generalized histologic phenomenon.     

心脏非粘液性原发肿瘤的病理学研究

我院１９６５年至１９９３年间，共检出心脏原发肿瘤２３６例，其中１６例为非粘液性肿瘤，占同期心脏原发肿瘤的６．８％。包括脉管瘤７例，间叶细胞瘤５例，间皮细胞瘤、脂肪瘤、横纹肌肉瘤及纤维弹力瘤各１例。良性和恶性肿瘤各８例。     

淋巴管瘤的超声特征分析

目的探讨淋巴管瘤的二维及彩色多普勒声像图表现特征。方法回顾分析30例淋巴管瘤患者的声像图资料,与手术病理资料对比分析,总结其特点。结果根据淋巴管瘤的发生部位将其分为疏松间隙处17例,体表软组织处10例及内脏处3例;按其病理分型分为囊性淋巴管瘤18例和海绵状淋巴管瘤12例;根据超声表现分为囊肿型23例,囊实混合型5例,强回声型2例。结论不同病理分型的淋巴管瘤其发生部位和超声表现有一定差异。超声检查对大多数淋巴管瘤的定位及定性诊断具有重要价值。     

肠系膜淋巴管瘤致小儿急腹症的诊治分析

目的 分析以急腹症为首发症状的小儿肠系膜淋巴管瘤的诊治特点.方法 回顾性分析2008年6月至2014年6月间收治的15例以急腹症为首发症状,最后经病理检查证实为肠系膜淋巴管瘤患儿的临床资料.结果 15例患儿中,男女比为4∶1,平均年龄3.9岁,无外伤史,部分发病前有饮食过量并剧烈运动的可疑诱因,均以急腹症就诊.腹痛史3 h～3年不等.本组门、急诊诊断准确率为26.7％(4/15),彩色超声诊断准确率为86.6％(13/15),CT检查诊断准确率为93.3％(14/15).所有病例均通过手术探查及病理诊断证实为肠系膜淋巴管瘤.其中肿瘤位于小肠系膜9例,结肠系膜6例.囊液清亮4例,乳糜样液体3例,血性液体8例.4例行完整的肿瘤剔除,6例部分剔除,5例连同累及肠管一并切除.全部患儿行彩色超声随访半年未见复发及粘连性肠梗阻发生,60％(9/15)随访3年以上未见复发.结论 肠系膜淋巴管瘤是一种临床少见的淋巴管先天性发育异常,缺乏特异性临床症状和体征,误诊及漏诊率高.对反复出现腹痛、腹胀的患儿应警惕患该病可能.彩色超声和CT检查对诊断帮助大,手术是有效的治疗手段,病理检查是诊断该病的金标准.     

肠系膜巨大淋巴管瘤1例

正患者男,54岁,发现腹部包块2年,于1周前出现无诱因餐前疼痛入院。体格检查:腹部正中可触及大小约15cm×15cm肿物,质韧,边界清,全腹无压痛、反跳痛及肌紧张。入院后CT全腹平扫示腹腔内软组织密度影,大小约56 mm×124 mm×150mm,CT值约为31 HU,边缘清晰,密度不均,其内可见散     

Spontaneous Regression of a Cystic Tumor in a Postpartum Woman; Is It A Cystic Lymphangioma?

Spontaneous regression of intra-abdominal cystic tumors in adults is unusual. Here, we present the case of an apparently spontaneous regression of a large intra-abdominal cystic mass found in the postpartum period of an 18-year-old woman. The regression was demonstrated using serial computed tomography (CT) examinations over a two-year period.