排序方式: 共有1条查询结果,搜索用时 0 毫秒
1
1.
Dr. P. C. M. Nair Yasser Wali Mathew Zechariah Zakia-Al-Lamki 《Indian journal of pediatrics》2001,68(10):995-997
Hemophagocytic lymphohistiocytosis (HLH) embraces the frequently indistinguishable conditions, namely familial hemophagocytic
lymphohistiocytosis (FHLH), sporadic hemophagocytic lymphohistiocytosis (SHLH) and virus associated hemophagocytic syndrome
(VAHS). The disease is very rare and invariably lethal. Evidence suggests that the disease may be due to an inherited defect
in immunoregulation that predisposes to an uncontrolled proliferation of activated histiocytes in response to a stimulus such
as viral infection. We report here a 3-day-old neonate with confirmed HLH who had a stormy course and a fatal outcome to the
disease process, in spite of early chemotherapy. To our knowledge, we believe this is the youngest reported case of HLH from
Middle East. No familial or infective cause could be attributed. 相似文献
1