肋骨骨化性纤维瘤的CT诊断

骨化性纤维瘤是一种骨组织的良性肿瘤,常见于青少年,颅面骨及四肢骨为其好发部位,发生于肋骨的骨化性纤维瘤较罕见,近年仅见个案报道~([1]).本文报道我院近4年经手术病理证实的肋骨骨化性纤维瘤7例,并结合文献进行分析.     

骨促结缔组织增生性纤维瘤的临床病理观察

目的:了解骨促结缔组织增生性纤维瘤的临床病理.方法:收集骨促结缔组织增生性纤维瘤1例和6例腹壁外韧带样纤维瘤病的临床资料.手术切除组织HE染色光镜观察.涂胶切片做Vimentin,Desmin,NF,S100蛋白的单克隆标记.结果:骨促结缔组织增生性纤维瘤的组织学改变和免疫组织化学标记与腹壁外韧带样纤维瘤病相似,临床症状和影像学改变与骨样骨瘤相似.结论:骨促结缔组织增生性纤维瘤易发生于青年男性,病理才能将其确诊,有复发的可能.     

股骨促结缔组织增生性纤维瘤1例

患者男,16岁,左大腿下段反复疼痛一年余,逐渐加重,活动后加剧,膝关节无明显活动受限.查体:大腿下段内侧可触及一肿块,质硬,活动度差,轻度压痛.实验室检查无异常.     

软骨黏液纤维瘤的X线诊断

目的:研究软骨粘液纤维瘤的X线表现。材料与方法:收集临床病理证实软骨黏液纤维瘤6例,其中男4例,女2例;年龄7～28岁,平均年龄16.5岁。全部病例术前拍摄X线片,其中1例CT平扫检查。结果:胫骨5例,股骨1例。5例发生于干骺端,1例位于骨干。病变均沿骨管轴生长。5例表现偏心性、膨胀性分叶状溶骨破坏,1例呈圆形。病变髓侧硬化边明显,2例皮质侧破坏,4例可见明显的分隔。6例均未见钙化存在。结论:X线检查对本病的诊断有重要作用。     

Proptosis in a young child

We encountered an extremely unusual presentation of proptosis in a 7-yr-old boy due to psammomatoid juvenile ossifying fibroma of frontoethmoidal region. The tumor also led to development of mucocele in the frontal sinus not yet fully developed as on opposite side.     

A huge unusual mass on the penile skin: Acrochordon

Acrochordons are flesh-coloured pedunculated lesions which occur in areas of skin folds. Although they are common in other sites of the body, we report the first case of huge penile acrochordon in the literature. Clinical, pathological and surgical findings of this lesion were presented and discussed.     

Congenital desmoplastic fibroma of the cranium

A case of congenital desmoplastic fibroma of the right parietal area between the two skull tables is presented.     

Neurofibromatosis 1 and osseous fibrous dysplasia in a family

We report on the consegregation of neurofibromatosis 1 (NF 1) and osseous fibrous dysplasia in a family. The father and 3 children by 2 women are affected. A fourth child had neither NF 1 nor osseous fibrous dysplasia. All 4 affected individuals had NF 1, i.e., caféau-lait spots in 4, neurofibromata in 4, Lisch nodules in 3, macrocrania in 3, scoliosis in 2, and curvature of the long bones in 2. Each demonstrated various fibroosseous lesions of the skeleton including non-ossifying fibromas in 3 and both non-ossifying fibromas and fibrous dysplasia in one. This pattern suggests that the fibrous bony lesions are a component of NF 1 in this family. Alternatively, a mutant gene resulting in the fibrous changes in bone could be linked to the gene for NF 1. Another possibility is the coincidence of the 2 non-linked traits segregating in the same family. © 1992 Wiley-Liss, Inc.     

Chondromyxoid fibroma of the foot

 Chondromyxoid fibroma is a rare benign cartilaginous tumour seen most frequently around the knee in children and young adults. Up to 17% occur in the foot, where more aggressive appearances have been reported. Four cases of chondromyxoid fibroma in the forefoot are presented, demonstrating the wide range of radiological appearances of this primary tumour. Three of the four tumours recurred, one at 19 years after surgery. These cases illustrate the need for thorough preoperative assessment to ensure complete surgical resection in an attempt to reduce the incidence of local recurrence.     

Chondromyxoid fibroma of the sternum

 We report the fourth case of chondromyxoid fibroma of the sternum described in the literature. The clinical, radiographic, pathologic and treatment aspects of this case are presented, and the literature on chondromyxoid fibroma in this unusual location is reviewed.