Odontogenic myxoma of the anterior mandible: Case report of a rare entity and review of the literature

This report intends to compare classic presentations of odontogenic myxoma in contrast to our case. We also suggest a comprehensive evaluation of lesions and strongly advocate against premature treatments before reaching a definitive diagnosis.     

儿童左手第二掌骨关节旁黏液瘤超声表现1例北大核心CSCD

患儿男,6岁,5个月前家属发现患儿左手掌包块,未就诊,1个月后包块逐渐增大;既往无特殊病史。查体:左手掌第二掌骨掌侧触及3.0 cm×2.0 cm×1.0 cm包块,质软,活动度尚可,局部无明显红肿及压痛,手指活动未见明显受限。实验室检查未见明显异常。左手掌超声:左手掌骨远端紧贴示指指屈肌腱见3.20 cm×1.32 cm×1.01 cm低回声肿物,形态欠规则,边界清,局部似见包膜,内部回声不均,可见条片状高回声及小灶性无回声(图1A),后方指屈肌腱略受压,周边及内部探及少许血流信号(图1B);考虑为滑膜来源腱鞘巨细胞瘤可能。行左掌肿物切除术,术中见肿物呈白色,包膜完整,与示指指屈腱粘连,实质内局灶呈胶冻样。术后病理:光镜下肿瘤细胞呈短梭形或星形,未见明显异型性,间质呈显著黏液变(图1C);诊断:(左手第二掌骨)关节旁黏液瘤(juxta-articular myxoma,JAM)。     

Mazabraud’s Syndrome

Teaching point: Mazabraud’s Syndrome defines the association of bone fibrous dysplasia and intramuscular myxoma, sometimes with pathological fractures or deformities in the lower limbs.