Ruptured abdominal aortic aneurysm in Marfan's syndrome

A rare case of ruptured abdominal aortic aneurysm in Marfan's syndrome is described. The patient was treated successfully with a straight aortic tube graft. Histology of the aneurysm wall showed changes typical of cystic medial necrosis.     

Ruptured abdominal aortic aneurysm: the persistent challenge

Despite improvement in anesthetic and postoperative care, ruptured abdominal aortic aneurysms (AAA) continue to have a high mortality. Thirty-three patients from 1980-1986 underwent surgery at West Virginia University for ruptured AAA, with 12 survivors (36.4 per cent). Age, use of MAST trousers, initial hemoglobin and blood pressure as well as operative time and estimated blood loss were not found to be significantly different between survivors and non-survivors. The blood pressure at the time of induction, during surgery, at the end of surgery, and the final temperature were significantly different. Our results show that the chance of survival is much greater if the patient responds to the initial fluid resuscitation prior to induction, and if blood pressure and temperature are maintained during the operation.     

主动脉弓部瘤及降部瘤的外科治疗

目的：总结主动脉弓部瘤及降部瘤的外科治疗经验。方法：4例主动脉弓部瘤及降部瘤患者,左心转流(LAV)3例,深低温停循环和选择性脑灌注(HCA SCP)1例。3例降主动脉瘤中,2例急诊在LAV下血管置换,1例择期在LAV下血管置换。1例弓部瘤急诊在HCA SCP下行半弓置换。结果：4例均无手术死亡及脊髓、肾脏损害,1例主动脉弓部瘤术后出现脑梗塞。结论：主动脉弓部瘤及降部瘤外科治疗中,选择正确的体外循环方法和适当的外科吻合技术对手术成功有重要的意义。     

Aortoplasty with pulmonary autograft patch for coarctation of the aorta combined with hypoplastic aortic arch in infant

<正>Objective To discuss the operative techniques and results of coarctation resection plus aortoplasty with pulmonary autograft patch for coarctation of the aorta combined with hypoplastic aortic arch in infant. Methods Between May 2007 and Dec 2009,14 cases including 9 males and 5 females with coarctation of the aorta and hypoplastic aortic arch underwent coarctation resection plus aortoplasty with pulmonary autograft patch in our     

电子束CT诊断主动脉弓离断及缩窄的优势

目的 探讨电子束CT诊断主动脉弓离断及缩窄的应用优势。方法 回顾性分析7例经临床确诊的主动脉弓离断或缩窄的相关诊断资料，讨论电子束CT诊断特点及优势。结果 EBCT图像可以清晰直观反映出病变类型、程度及并发的其它畸形，7例中主动脉弓离断4例（均为A型），主动脉缩窄3例（位于主动脉峡部），对于离断或狭窄的诊断，EBCT的准确率为100％，超声有2例漏诊（1例离断，1例缩窄），1例不能肯定诊断。7例中合并室间隔缺损6例，房间隔缺损1例，动脉导管未闭5例，三房心1例。结论 电子束CT诊断主动脉弓离断或缩窄直观、真实、准确，且全面快捷无创，可作为此类疾病的首选检查方法，一定程度上能够取代传统血管造影。     

电子束CT诊断主动脉弓离断及缩窄的优势

目的 探讨电子束CT诊断主动脉弓离断及缩窄的应用优势.方法 回顾性分析7例经临床确诊的主动脉弓离断或缩窄的相关诊断资料,讨论电子束CT诊断特点及优势.结果 EBCT图像可以清晰直观反映出病变类型、程度及并发的其它畸形,7例中主动脉弓离断4例(均为A型),主动脉缩窄3例(位于主动脉峡部),对于离断或狭窄的诊断,EBCT的准确率为100%,超声有2例漏诊(1例离断,1例缩窄),1例不能肯定诊断.7例中合并室间隔缺损6例,房间隔缺损1例,动脉导管未闭5例,三房心1例.结论 电子束CT诊断主动脉弓离断或缩窄直观、真实、准确,且全面快捷无创,可作为此类疾病的首选检查方法,一定程度上能够取代传统血管造影.     

Pseudo-pseudo-hypoparathyroidism with coarctation of the aorta—a clinical syndrome?

Two cases of pseudo-pseudo-hypoparathyroidism are described, associated with coarctation of the aorta, suggesting a further common clinical link (besides those already recognized) between the former condition and Turner''s syndrome. The need for a change of nomenclature of pseudo-pseudo-hypoparathyroidism is emphasized.     

主动脉峡部环扎构建猪导管前型主动脉缩窄模型

目的建立主动脉峡部环扎构建猪导管前型主动脉缩窄模型。方法将10头猪麻醉后,经左侧第三肋间开胸,使用聚对二氧环己酮单丝可吸收缝线环绕主动脉峡部,固定其直径,测定主动脉峡部直径及跨主动脉峡部的收缩压差值（△P）。8周后,行心导管介入术,再次测定主动脉峡部直径及△P,用球囊导管对主动脉峡部进行扩张。结果8周后,2头动物主动脉峡部直径增大,未测得△P;建模成功率为80％。建模成功的8头动物,在心导管介入术时的体质量明显高于建模前,差异有统计学意义（P〈0．01）;球囊扩张术后的△P显著高于建模前,差异有统计学意义（P〈0．01）;但球囊扩张术后主动脉峡部内径无明显增大,差异无统计学意义（P〉0．05）。结论成功建立了主动脉峡部环扎构建猪导管前型主动脉缩窄模型的方法。