Uterine leiomyosarcoma: report of seven cases and review of the literature

We report 7 cases of leiomyosarcoma of the uterus observed in the obstetrical and gynaecological department of Sfax (Tunisia). It's a rare tumour with difficult diagnosis and poor prognosis. It requires mainly a surgical treatment and radiotherapy.     

Retroperitoneal paraganglioma: case report

Paraganglioma are rare neoplasms arising from undifferentiated cells of the primitive neural crest. We report a case of a 53 years old patient presented with a large tissular retropéritoneal tumour situated above the left kidney. Serum Adrenaline, Nor drenaline and VMA levels were normal. Surgical complete resection of the tumour was performed without intra-operative incident. The histopathological examination and the immunohistochemical analyses concluded to a non secreting retroperitoneal paraganglioma. Postoperative course was uneventful.     

Gastric leiomyosarcoma: two unusual cases

Two cases of gastric leiomyosarcoma, which presented unusually with lower abdominal masses, are described. The difficulties in the preoperative diagnosis of this rare malignancy are discussed.     

腹膜后异位妊娠1例病例报告

异位妊娠是一种常见的妇科急症,由于内出血严重,可能危及孕妇生命,是妊娠所致死亡的主要原因之一.腹腔妊娠常因缺乏典型临床症状,易被忽视和误诊[1].其中腹膜外异位妊娠作为一种腹腔妊娠类型,十分罕见[2].我院近期收治1 例妊娠组织种植于腹膜和直肠间隙之间的患者,现将病例报道及文献复习如下.     

后腹腔镜肾蒂阻断下保留肾单位肾肿瘤手术(附6例报告)

目的 探讨后腹腔镜肾蒂阻断下保留肾单位治疗肾肿瘤的方法及手术技巧. 方法收治肾脏外生性实体肿瘤6例患者,其中.肾细胞癌2例,肿瘤直径分别为2.5 cm和2.2 cm;肾错构瘤4例,肿瘤直径为2.5～3.5 cm.经后腹腔镜径路在自制的肾蒂阻断装置中阻断肾蒂,做保留肾单位的肾肿瘤手术,术中距肿瘤0.5～1.0cm处行肾脏部分切除术,创面缝合止血.结果 6例手术均成功,手术时间120～210min,中位数150min.术中出血150～200ml,中位数170ml.肾蒂血流阻断时间18～33 min,中位数22 min.2例肾细胞癌术后切缘阴性.术后随访6～12个月,未见肿瘤残留及复发.结论 后腹腔镜肾脏部分切除术中应用自制的肾蒂阻断装置,具有良好的止血效果、手术创伤小、视野清晰、操作方便、能最大限度地保留患肾等优点,术后恢复良好.     

Retroperitoneal ganglioneuroma. A case report

BACKGROUND: Ganlioneuroma is a rare, benign, neurogenic tumor originating from the neural sheath and frequently localized in the retroperitoneum. AIM: Report of a new case. CASE: We report a case of a 36-year-old woman presenting isolated right lumbar pain. Computed tomography revealed a heterogeneous, right, retroperitoneal mass, 13 cm in diameter. Complete resection of the tumor and right nephrectomy were performed. Histology confirmed the diagnosis of ganglioneuroma. Follow-up was 10 months with no recurrence. Through this case, we discuss diagnostic, therapeutic and prognostic aspects of this disease.     

急性羰基镍中毒3例报告

3例均于生产中发生中毒 ,主要为肺损伤 ,经糖皮质激素、吸氧等治疗 ,痊愈     

新生儿腹膜后淋巴管瘤并文献复习

目的探讨新生儿腹膜后淋巴管瘤的临床特点与诊治策略。 方法选择2017年7月3日，因"生后腹胀31 min"收入成都市妇女儿童中心医院新生儿科，并确诊的1例腹膜后淋巴管瘤新生儿为研究对象。回顾性分析该例新生儿的临床病例资料，总结其临床特点和诊治经过，并进行相关文献复习。本研究对新生儿腹膜后淋巴管瘤相关文献的检索策略为：以"淋巴管瘤""腹膜后淋巴管瘤""淋巴管畸形""新生儿""lymphangioma""retroperitoneal lymphangioma""lymphatic malformation"及"neonate"为关键词，检索中国知网数据库、PubMed等国内外文献数据库建库至2018年12月，收录的关于新生儿腹膜后淋巴管瘤的文献，并总结该病临床特点和诊治方案。本研究符合2013年修订的《世界医学协会赫尔辛基宣言》要求。 结果本例患儿为女性，入院诊断为腹腔积液待查；入院年龄为生后31 min，其病史采集与诊治过程如下。①病史采集：生后腹胀。母亲于孕龄分别为24、40孕周时，接受产前胎儿超声检查均提示胎儿腹腔见囊性占位、腹腔大量积液。患儿出生后除腹胀、腹围进行性增加外，无其他明显异常表现。生后2 d内对该例患儿行腹腔穿刺2次，均抽出较多淡黄色液体，腹水检查结果显示为渗出液。腹部X射线摄片、超声及CT检查，均显示腹腔囊性占位、腹腔大量积液。②手术、治疗经过及转归：患儿在全身麻醉下，共计进行3次手术，具体如下。第1次，于生后第3天对其进行腹腔镜探查术及淋巴液漏口结扎术，术中清理腹腔淡黄色清亮液体约600 mL，手术后有明显的淋巴液漏，腹腔引流液量大，平均为127.2 mL/d，并且患儿出现营养不良表现。第2次，于生后第28天对其进行腹膜后肿物切除术，术中切除淋巴管样异常增生病灶送组织病理学检查结果显示，"左侧腹膜后肿物符合淋巴管瘤"，术后腹腔引流液量明显减少，但患儿腹胀进行性加重，随访腹部超声检查提示，腹膜后淋巴管瘤复发，弥漫性并逐渐增大。第3次，于生后第49天对其进行剖腹探查术的结果显示，结肠相关广泛淋巴管畸形(LM)伴大范围淋巴液回流障碍，形成弥漫性混合型淋巴管瘤，因此进行结肠次全切除术、腹膜后淋巴管瘤部分切除术，术后腹腔引流液量少，无腹胀发生。第3次手术后14 d，对该例患儿再次开始脱脂奶粉喂养，并且顺利增加至全肠内营养。患儿总住院时间为81 d，治愈出院，随访至18个月龄，患儿生长发育良好，随访腹部影像学检查结果显示，腹膜后淋巴管瘤未复发。③文献检索结果：仅检索到2例新生儿腹腔淋巴管瘤的文献报道。其中，1例为腹腔脐部至右侧腹股沟区的表浅巨囊型淋巴管瘤，因无腹腔脏器受压迫的临床表现，而对其采取生后保守观察，3岁时淋巴管瘤缩小，接受激光治疗；另一例为腹膜后淋巴管瘤，因腹胀明显，于生后第10天对其采取淋巴管瘤手术全切除术。这2例患儿均预后良好。 结论新生儿淋巴管瘤根据其部位、大小和临床表现，选择合适的干预时间和方式，能取得较好的治疗效果及远期预后。     

A case report of leiomyosarcoma of the inferior vena cava

A case of leiomyosarcoma of the I.V.C. is described, with emphasis on the CT appearance. CT is useful for the diagnosis and follow up on this case.     

Primary leiomyosarcoma of the vagina. Case report and literature review

BACKGROUND: The vast majority of primary vaginal cancers are squamous cell carcinoma. The leiomyosarcoma of the vagina is extremely rare neoplasm. It comprising 2% to 3% of vaginal malignancies. Only 77 cases have been reported up to date in Anglo-Saxon literature . AIM: Report of a new case CASE: We report a case of a patient 43 years old, single and presented a tumor of 7 cm to the detriment of the posterior wall of the vagina. The treatment consisted of a radical colpohysterectomy followed by postoperative radiotherapy. After 40 months, she is still alive without local or distant recurrence. CONCLUSION: This is a rare observation. The surgery is the basic treatment, the poor prognosis of these tumors remains linked especially to the histological grade.