Olivopontocerebellar atrophy in a young patient: A case report with radiologic findings

BackgroundOlivopontocerebellar atrophy (OPCA) is a term that encompasses an increasing number of neurodegenerative syndromes that lack a unique pathogenesis but are known to result from a disruption in the relationship between the cerebellar cortex, dentate nucleus, and the inferior olivary nuclei. OPCA can be difficult to diagnose on clinical grounds only and recent data suggests that OPCA affects 3–5 individuals in every 100,000 and may constitute almost 6% of patients diagnosed with atypical parkinsonism.Case reportHerein, we report the case of a 36-year-old female that initially developed dysarthria and gait abnormalities and subsequently presented with progressive neurologic signs and symptoms. A routine MRI of the brain was performed and high-resolution images were taken through the entire posterior fossa which showed prominent widening of the CSF spaces in the posterior fossa, cerebellar atrophy and reduction in the size of the pons, consistent with a diagnosis of OPCA.ConclusionOlivopontocerebellar atrophy is challenging condition to diagnose on a clinical basis, and hence requires corroboration of clinical and physical examination findings with radiologic findings. MRI of the brain is the gold standard in assessing OPCA and is an extremely valuable imaging modality in distinguishing OPCA from other neurological disorders and allows for the precise determination of OPCA subtypes.     

原发性肺淀粉样变的CT表现

淀粉样变性是一组蛋白质以异常的纤维结构沉积于细胞之间,该类纤维接触硫和碘会出现和淀粉一样的反应,故命名为淀粉样变性.原发性呼吸系统淀粉样变是指在无系统淀粉样变的情况下,淀粉样物质在呼吸系统沉着.本病为少见疾病,临床表现多种多样且无明显特征性,本文收集原发性肺淀粉样变5例,并结合文献,探讨其影像学表现.     

A case with primary cardiac paraganglioma: imaging findings

A 67-yeary-old middle-aged woman admitted to the hospital with chief complaints of intermittent palpitation, fatigue for more than 3 months, and bilateral lower extremity edema about 2 months. A solid mass was discovered in the right atrium by echocardiographic examination, and computerized tomography (CT) guided needle biopsy of the mass was performed and revealed a neurogenic tumor, which was a paraganglioma. She underwent surgical excision of the tumor and had uneventful recovery at a month post-operation.     

Imaging findings of primary well-differentiated liposarcoma of the liver: a case report

Primary liposarcoma of the liver is extremely rare. We report here on a case of primary well-differentiated liposarcoma in the left hepatic lobe of a 63-year-old woman. Abdominal ultrasonography showed a well-defined, echogenic, round mass. Abdominal computed tomography (CT) and magnetic resonance (MR) images showed an almost fatty, lobulated mass with a few, random distributed vascular structures and a small area of nodular enhancement. The resected tumor appeared as a well-defined, round, tan-yellow mass. Histological analysis showed a well-differentiated liposarcoma.     

Radiological findings of primary localized amyloidosis of the ureter

Localized amyloidosis is a rare condition, especially that involving the ureter. Because of its rarity and the difficulty in differentiating this condition from urothelial carcinoma by intravenous urography and computed tomography, nephroureterectomy has often been performed unnecessarily for this disease. The authors encountered two cases of this disease, both of which showed a negative urine cytology, no obvious mass effect, and a hypointensity on T2-weighted imaging. Because these findings are very rare in urothelial carcinoma, ureteroscopy-guided biopsy was performed, which yielded the diagnosis of amyloidosis. The patients were then treated and followed up at our institute. Primary localized amyloidosis of the ureter should be considered when evaluating ureteric lesions visualized as hypointensities on T2-weighted images that do not show an obvious mass effect, which could help in the avoidance of unnecessary surgery.     

Imaging findings in primary adenosquamous carcinoma of the liver: a case report

Adenosquamous cell carcinoma is characterized by both squamous and glandular components, and is a rare disease of the liver that is the subject of few reports in the literature. We present a case in which the imaging findings on CT, MRI, and hepatic arteriography, as well as pathological correlation of the tumor and the clinical history, aided in including this entity in the differential diagnosis.     

Scintigraphic findings in primary amyloidosis of the heart and stomach

The effectiveness of scintigraphic studies in the study of patients with primary systemic amyloidosis has not been reported previously. This case report describes a patient with the scintigraphic findings of thickened myocardium and delayed gastric emptying, which correlated well with the presence of amyloid deposits in these organs at autopsy. Additionally, the liver and spleen had normal scintigraphic appearances and were free of amyloid at autopsy. Radionuclide studies appear useful in assessing the anatomic and physiologic abnormalities assessed by amyloid deposition.     

肺淀粉样物质沉积症影像表现一例

本文报道肺淀粉样物质沉积症影像表现1例。患者,男,61岁,胸部CT表现为右肺下叶后基底段团块样占位影,大小约30 mm×40 mm,边界清楚,边缘不规则,密度均匀,CT值约43 HU,增强扫描未见明显强化。病理诊断:考虑肺淀粉样物质沉积症。     

Hepatic hemangioma presenting atypical radiologic findings: a case report

A 69-year-old woman was referred to our hospital due to a liver tumor that was incidentally noted on ultrasound (US). US revealed a pedunculated mass of 5 cm in diameter, with a heterogeneous echo pattern. On arterial phase dynamic contrast-enhanced computed tomography (CT), a tiny enhancing dot in the upper aspect of the mass was seen; whereas, the main portion of the lesion appeared as hypoattenuating. The tumor was of low intensity on T1-weighted magnetic resonance (MR) images, and showed slightly heterogeneous high intensity on T2-weighted MR images. The most characteristic feature of the tumor was its exophytic appearance. On post-gadolinium hepatic arterial dominant-phase MR images, the tumor showed nodular enhancement centrally, with progressive spread of enhancement on later images. Angiography showed dilatation of the right posterior inferior branch of the hepatic artery and C-shaped opacification. Since we could not rule out malignancy for these nonspecific radiologic findings, a partial resection of the liver was carried out, resulting in a pathological diagnosis of hepatic hemangioma. This hemangioma had marked hyalinization and fibrosis, causing a heterogeneous appearance on MR images. The tumor presented an exophytic appearance, which caused some diagnostic confusion.     

原发性肺非何杰金淋巴瘤的影像诊断

目的：研究原发性肺淋巴瘤的影像诊断，方法：7例均经病理和临床证实的原发性肺非何杰金淋巴瘤，均作X线胸片、腹部B超检查，其中5例作胸部CT。结果：6例单发和1例多发性结节(两肺各一灶)或肿块，病变分布无肺叶偏向，病灶密度较低而不均。6个病灶边缘毛糙不规则，1个病灶边缘光整，另一个病灶边缘部分光整，其中2个病灶边缘分叶，2个病灶见长短毛刺。1个病灶见空洞。作胸部CT的5例均见空气支气管征。其中1例伴纵隔淋巴结肿大，5例合并肺叶或肺段的肺不张或部分肺不张，3例侵犯胸壁伴少量胸水。结论：原发性肺淋巴瘤的影像表现多样，非特异性，常见有空气支气管征的边缘毛糙的结节或肿块。本病应与肺癌、隐源性机化性肺炎鉴别，最后定性诊断需病理检验证实。     

Colorectal hemangioma: radiologic findings

The authors correlated radiographs with the clinical and histologic data of 12 patients with colorectal hemangioma. All patients presented with rectal bleeding, which was chronic in seven. Phleboliths were also visible in seven cases, which correlated with chronic bleeding in five. On barium studies, three masses were soft and three produced rigid narrowing. The atypical features of rigid luminal narrowing, which might mimic a carcinoma, and hypovascularity correlated with chronic bleeding or visible phleboliths, which suggest the correct diagnosis of colorectal hemangioma.