神经纤维瘤病的眶面部影像学表现：附11例报告

目的：探讨神经纤维瘤病在眶面部的ＣＴ表现。材料和方法：总结分析了１１例经手术病理证实的神经纤维瘤病在眶面部的Ｘ线平片和ＣＴ表现。结果：本病的典型Ｘ线表现是眶骨骨质缺损和眼眶扩大，并可形成空眶征和立卵形扩大。ＣＴ表现为：（１）丛状神经纤维瘤病（６例），表现为周界不清楚、形状不规则的软组织影，颞肌和眼睑肌及眼直肌增粗变形；（２）眶骨发育不全（８例）；（３）眼眶内肿瘤（５例）；（４）眼积水（２例）。一个患者可有上述一种甚至四种表现。结论：ＣＴ能直接全面地显示神经纤维瘤病在眶面部的表现及眼眶与颅脑的交通，并能明确病变的范围和程度，为手术和临床治疗提供指导性意见。     

主动脉窦瘤X线征象与造影表现及其在治疗中的意义

主动脉窦瘤Ｘ线征象与造影表现及其在治疗中的意义蒋瑾主动脉窦瘤又称Ｖａｌｓａｌｖａ＇ｓ窦瘤，窦瘤破裂后导致急性心功能不全，及时评价Ｘ线征象与主动脉造影表现，对治疗有明显帮助。作者通过分析我院近１０年共收治７例主动脉窦瘤病例，讨论Ｘ线平片与造影表现对治疗...     

正常腕关节X线测量

正常腕关节Ｘ线测量朱建民金宗达陈新刚张庆宏某些腕关节及其周围病变和损伤可导致腕关节形态学改变，测量正常腕关节Ｘ线片有关参数有助于这些疾病和损伤的诊断和疗效的评定。笔者采用标准Ｘ线摄片技术，报告２００个（１００人）正常腕关节Ｘ线正、侧位片有关参数的测量...     

骨肉瘤病的影像学诊断

目的分析骨肉瘤病的影像学表现，评价影像学的诊断价值。方法总结分析15例骨肉瘤病的影像学特点。15例均行平片检查，其中13例行CT检查，11例行发射型计算机体层摄影(ECT)检查，5例行MR检查。4例行DSA造影检查。结果15例中骨肉瘤病主病灶位于股骨远端者8例，胫骨近端5例，肱骨近端1例，锁骨1例。主病灶之外的多发病灶发生在股骨远端者6例，其中双侧病变2例。位于胫骨近端者8例，骨盆2例，脊柱椎体6例，颅骨1例，髂骨及骶髂关节4例，双侧股骨近端3例，胫骨远端2例。15例主要病变X线表现为典型骨肉瘤样，而发生在其他部位的病灶表现不同，多呈圆形成骨样改变。13例CT观察到病变范围分布及软组织肿块的情况；其中发生在骨髓病变区内的病变多为边缘清楚的高密度瘤骨，5例病变在MRI呈圆形信号改变。特别是髓腔内低信号的骨化区域显示得很清楚。11例ECT检查者可见呈全身分布的广泛浓聚区域。4例于DSA可观察到肿瘤血管边界及肿瘤血管的走行。结论骨肉瘤病为全身的多发病灶，影像学检查可观察全身发病的部位、表现，对疾病的诊断和治疗将提供可靠的依据。     

滑膜骨软骨瘤病X线诊断（附61例报告）

滑膜骨软骨瘤病Ｘ线诊断（附６１例报告）高士伟，王学庆，孙家永滑膜骨软骨瘤病为发生于关节囊、滑囊及腱鞘滑膜的良性病变，笔者搜集６１例，３０例经手术与病理证实。现着重Ｘ线诊断探讨如下。一、一般资料：作者单位：２７６００３山东省临沂地区医院放射科６１例中男...     

皮肤粘膜淋巴结综合征胸部的X线表现（附50例分析）

本文报导５０例皮肤粘膜淋巴结综合征的Ｘ线表现，是以肺间质的病变为主，肺门及肺纹理的改变是最基本的Ｘ线表现，若患儿伴有皮肤粘膜损害和心脏改变，诊断不难确立，作者体会通过该综合征的再识认有利于Ｘ线诊断拓宽思路，密切结合临床资料，实验检查，心电图及Ｂ超，小儿胸片短期复查，动态观察，最终提高Ｘ线诊断正确率。     

创伤性湿肺的X线诊断（附100例分析）

本文报告１００例创伤性湿肺的临床资料。结合文献，探讨了创伤性湿肺的形成原因，Ｘ线表现、Ｘ线分型及鉴别诊断。认为其形成原因系多种因素并存。Ｘ线表现是肺挫伤和肺裂伤的复合改变。“面纱症”是创伤性湿肺的特征性Ｘ线表现     

滑膜骨软骨瘤病中游离体表现与诊断关系

分析滑膜骨软骨瘤病中游离体Ｘ线、ＣＴ表现，讨论游离体发生与诊断本病关系。材料与方法回顾分析２３例关 ，外游离体的Ｘ线ＣＴ表现，并与病理对照。２３例摄Ｘ线平片，其中１３例ＣＴ扫描，有６例作高分辨率ＣＴ扫描。２２例手术病理证实，另１例关节镜检查病理证实。结果关节内、外游离体钙化程度和形态大小与游离体形成时间有关，也与病程有关。往往病程长，关节内外游离体数目多，钙化与骨化明显，且偏大并累及范围广，反之，     

结核性与其它气管、大支气管广泛性病变的X线诊断与鉴别诊断

目的：为提高对支气管结核与其它疾病引起的气管、大支气管广泛性病变的临床、Ｘ线诊断与鉴别诊断水平。方法：分析已明确诊断的各种导致气管、大支气管广泛性狭窄的疾病２５例，其中气管、大支气管结核８例、气管恶性肿瘤７例、淀粉样变性３例、复发性多软骨炎２例、胸内剑鞘状气管５例的临床与Ｘ线表现。结果：发现除大部分疾病有某些Ｘ线特征外，其余均有类似的Ｘ线表现。结论：导致气管、大支气管广泛性狭窄的疾病，某些有类似的Ｘ线表现，需要结合临床与它其检查进行综合分析，才能得到正确的诊断与鉴别诊断     

Ⅰ型高雪病的影像诊断（附一例报告及文献复习）

目的 提高对Ｉ型高雪病骨骼系统改变影３像学表现的认识。方法 报告１例Ｉ型高雪病的Ｘ线平片和ＭＲ所见，并作文献复习。结果 本病的Ｘ线平片有特征性改变，ＭＲＩ既能显示骨骼病变从向累及范围，又能观察骨髓内部受累的变化。纣化 ＭＲＩ是诊断高雪病骨骼受累的最佳方法。     

Isolated hepatic hemangiomatosis in adults: Report of two cases and review of the literature

Hepatic hemangiomatosis is a rare condition characterized by diffuse replacement of liver parenchyma with tissue similar to that of cavernous hemangioma. The purpose of this report is to illustrate two adult cases of hepatic hemangiomatosis and to review the pathological, radiological and clinical issues of this condition. The first case is that of a 47-year-old woman with extensive involvement of the entire liver. The right lobe was almost totally replaced, and only a limited amount of residual hepatic parenchyma was present in the left lobe. The second case is that of a 31-year-old woman with less extensive involvement. The right lobe was almost totally involved, and was accompanied with a large hematoma. The left lobe was relatively unaffected. Both cases were complicated by consumption coagulopathy (Kasabach–Merritt syndrome). The patients were successfully managed surgically, with living donor liver transplantation in the first case and extensive right lobectomy in the second case. The condition described by the term hepatic hemangiomatosis includes a wide clinical spectrum, with some cases asymptomatic, some accompanied with shunting, and some resulting in rupture or life-threatening hepatic failure. The disease has a good overall prognosis, with surgery and arterial embolization as effective treatment options.     

Case report 671

Since extensive involvement of the lower extremity with arteriovenous malformations occurs often combined with the potential risk of hemorrhage, transcatheter embolization has become an attractive alternative to surgical resection [7, 9]. We describe an unusual case of extensive intraosseous hemangiomatosis, with a concomitant arteriovenous malformation that presented in a 35-year-old woman as synovitis in a knee. MR images demonstrated that the lesion was far more extensive than originally suggested and directed the subsequent biopsy and embolization. The differential diagnosis was discussed and the subject of intraosseous hemangiomatosis with associated AVM was considered in some detail.     

先天性骨梅毒的X线表现(附5例报告)

目的:探讨先天性骨梅毒的X线表现。方法:回顾性分析5例先天性骨梅毒患儿的骨骼X线平片及临床表现。结果:先天性骨梅毒的X线表现主要包括:①干骺端炎,呈多发、对称性分布,可为先天性骨梅毒最早出现的征象;②骨干炎(骨髓炎);③骨膜炎,是最常见的征象。结论:X线检查对发现和诊断婴幼儿骨梅毒病变有非常重要的意义,有时可以在临床症状出现之前显示骨梅毒的改变,为临床早期诊断提供线索。     

Lung scintigraphy in pulmonary capillary hemangiomatosis. A rare disorder causing primary pulmonary hypertension.

The authors report the results of lung scintigraphy in two patients with primary pulmonary hypertension caused by pulmonary capillary hemangiomatosis, a rare disorder resulting from the proliferation of histologically normal capillaries in the lung. Perfusion studies revealed a nonhomogeneous pattern with some focal defects, similar to that seen with some other histologic types of primary pulmonary hypertension. The mechanisms underlying this perfusion pattern are unknown.     

Diffuse neonatal hemangiomatosis: CT findings in an adult.

Diffuse neonatal hemangiomatosis (DNH) is a rare disorder that usually presents in infancy and has a high mortality rate. We report a long-term adult survivor of DNH who presented with multiple calcifications in the bowel wall, liver, spleen, and adrenal glands on CT. Diffuse neonatal hemangiomatosis needs to be added to the causes of visceral calcifications.     

儿童H5N1型禽流感病毒性肺炎的胸部X线表现(附确诊及疑似病例各一例)

目的 描述儿童高致病性H5N1型禽流感病毒性肺炎患者的胸部X线表现。方法 回顾性分析1例经世界卫生组织确认为H5N1型禽流感病毒感染患者及1例疑似患者的胸部X线表现。结果 2例患者的胸部X线表现特点为：两肺大致对称、广泛分布的团絮状及大片状渗出病变，密度较高，边缘模糊；动态观察短期内病灶形态变化快，呈游走性；后期遗留纤维化病变。结论 儿童高致病性H5N1型禽流感病毒性肺炎的动态胸部X线表现具有定特征性。熟悉其胸部X线表现有助于该病的诊断，但最终确诊须依靠流行病学史及实验室检查。     

Diffuse neonatal hemangiomatosis: imaging findings in two patients.

Diffuse neonatal hemangiomatosis is a rare condition in which cutaneous and visceral hemangiomas may coexist. Intra-abdominal involvement occurs commonly and, if untreated, may result in high-output cardiac failure and other life-threatening conditions. We report two neonates with this disease and discuss the radiographic findings and the role of vascular embolization in the treatment of hepatic hemangiomatosis.     

Diffuse pulmonary hemangiomatosis

The authors describe three pediatric patients with diffuse pulmonary hemangiomatosis. Virtually identical clinical, radiographic, and pathologic findings were observed in each case. The combination of diffuse interstitial pulmonary infiltration and bloody pleural effusion in a child is pathognomonic. Early recognition of hemangiomatosis can allow more effective evaluation of therapeutic measures.     

骨非骨化性纤维瘤的X线诊断（附16例报告）

目的：探讨非骨化纤维瘤的X线诊断及鉴别诊断。方法：分析X线资料完整并经手术病理证实的非骨化性纤维瘤16例,其中CR片10例、常规X线片6例。结果：全组病例X线表现均较典型,凭X线检查基本可以术前作出诊断。但应注意与一些X线表现类似的疾病相鉴别。结论：优质X线片特别是图像清晰的CR片能真实的显示病变的特征,有助于确诊,当然,定性诊断须依赖于病理检查。