Uterus didelphys with obstructed hemivagina and ipsilateral renal agenesis

This is a case report of twoo patients how have uterus didelphys with obstructed hemivagina and ipsilateral renal agenesis with different clinical manifestations. Progressive abdominal pain after menarche, anuria or obstipation with the existing paravaginal tumor indicates this rare anomaly. Initially, the anomaly remains unrecognized, while patients most frequently refered to surgeons for assistance. The method of choice for diagnosis is clinical examination, ultrasonography and magnetic resonance (MR) imaging. Transvaginal excision of the septum is appropriate mode of treatment.     

Uterus didelphys with a blind hemi-vagina and homolateral renal agenesis

The authors report a case of bicervical bicornuate uterus with a blind hemi-vagina associated with homolateral renal agenesis. A review of the embryology and the various etiopathogenic theories for this rare anomaly are presented and the therapeutic principles are discussed.     

Uterus didelphys with an obstructed hemivagina and ipsilateral renal agenesis: a rare cause of acute abdomen in pubertal girls.

The unique clinical syndrome of uterus didelhphys with an obstructed hemivagina and ipsilateral renal agenesis, presenting as acute abdomen in three pubertal girls, is reported. Accurate preoperative diagnosis and appropriate treatment will offer relief of symptoms and decrease morbidity and unnecessary procedures.     

Acute urinary retention secondary to uterus didelphys with imperforate vagina

Cyclic dysmenorrhea, unilateral abdominopelvic mass, acute urinary retention and renal agenesis ipsilateral to the pelvic mass in a young woman suggest uterus didelphys with unilaterally imperforate vagina.     

Endoscopic septotomy: a new surgical approach to infantile hydrometrocolpos with imperforate hemivagina and ipsilateral renal agenesis

The authors propose a new surgical approach for neonates and infants with hydrometrocolpos caused by double vagina and imperforate hemivagina. Usually for these patients, laparotomy is a common approach used to decompress the obstructed hemivagina. The authors compared the characteristics of three options used to relieve obstruction of the hemivagina using endoscopic, transvaginal, and laparotomy approaches. An endoscopic septotomy (colposcopic approach) using the Storz neonatal resectoscope is less invasive and less expensive than other methods. We emphasize that endoscopic septotomy is a feasible surgical method to relieve the obstructive symptoms related to imperforate hemivagina.     

Unilateral renal agenesis with or without ipsilateral adrenal agenesis

We analyzed 7 patients with unilateral renal agenesis. The coexistence of unilateral renal agenesis with ipsilateral adrenal agenesis was confirmed surgically in 2 patients, 1 of whom had clinical features of Cushing's syndrome owing to adrenocortical adenoma of a solitary adrenal gland. It is imperative to suspect abnormalities of the ipsilateral adrenal gland when unilateral renal agenesis is encountered. Unilateral renal agenesis usually is asymptomatic. Recognition of this anomaly is essential for early correct diagnosis.     

Seminal vesicle cyst associated with ipsilateral renal agenesis

A case of seminal vesicle cyst associated with ipsilateral renal agenesis was experienced recently in our clinic. A 23-year-old male presented with a complaint of right hemiscrotal pain. Right kidney was not visualized by excretory urography. Cystoscopic examination revealed the absence of the right half of trigone and the right posterolateral wall bulging into the bladder, suggestive of an extrinsic mass displacing the bladder wall. Ultrasonography and computerized tomographic scan showed a large cystic mass in the right side of the retrovesical region. Exploratory operation disclosed that the cystic mass was part of the dilated seminal vesicle. Seminal vesiculectomy was done. Many cases of seminal vesicle cyst are associated with a simple or complex malformation of ipsilateral upper urinary tract (renal agenesis, dysplasia, hypoplasia and ectopic ureter). We speculate that most of the benign seminal vesicle cysts are formed as a congenital anomaly due to defective mesonephric duct development which causes concomitant malformations in the upper urinary tract.     

Seminal vesicle cyst associated with ipsilateral renal agenesis

Seminal vesicle cysts present at the age of high sexual activity. They manifest with symptoms of bladder irritation and pain on ejaculation. They arise because of congenital obstruction of ejaculatory duct. Diagnosis can be made by careful rectal examination supplemented by an intravenous urogram, cystogram, seminal vesiculogram, and cystoure throscopy. Surgical excision of the cyst is the definitive treatment. We present a case (fright seminal vesicle cyst associated with ipsilateral renal agenesis, with a review of the= pertinent literature.     

Seminal vesicle cyst and ipsilateral renal agenesis

A case of seminal vesicle cyst with ipsilateral agenesis is presented. The embryologic events, clinical symptoms, and diagnosis are discussed, emphasizing the value of sonography and computer tomography in identifying the cyst. Surgical resection is the treatment of choice.     

Gartner''s duct cyst and ipsilateral renal agenesis

A child with unilateral renal agenesis was found by routine vaginoscopy to have a large ipsilateral Gartner's duct cyst. The cyst was marsupialized into the vagina. Embryogenesis of a Gartner's duct cyst and associated renal agenesis is discussed.     

Seminal vesicle cyst and ipsilateral renal agenesis

A case of seminal vesicle cyst and ipsilateral renal agenesis is presented, the literature summarized, the embryology reviewed, and the differential diagnosis discussed. Our reasons for surgical therapy are stated.     

Prognosis of patients with unilateral renal agenesis

The clinical course was reviewed in 157 patients with unilateral renal agenesis and a normal contralateral kidney for the purpose of establishing a prognosis. There were 85 males (54%) and 72 females (46%). The mean age at diagnosis of unilateral renal agenesis was 37 years. The mean years at risk was 56. Proteinuria (>150 mg/24h) was found in 19% of the 37 patients tested (P<0.001), hypertension developed in 47% of the 47 patients tested (P=0.010), and renal function (adjusted for age and sex) was decreased in 13% of the 32 patients tested (P=0.001). An increased filtration fraction was found in 7 (54%) of 13 patients evaluated. At the completion of this study, 114 patients (73%) were alive, and the survival rate was similar to that of age-, sex-matched United States life tables. Forty-three patients (27%) died; 6 deaths (4%) were caused by renal failure. Our review indicates that patients with unilateral renal agenesis and a normal solitary kidney are at increased risk of proteinuria, hypertension, and renal insufficiency. Therefore, it is essential to have prolonged and careful follow-up and to employ strategies that maximize renal preservation.     

Skeletal anomalies associated with unilateral renal agenesis

Unilateral renal agenesis is sometimes associated with skeletal anomalies. The skeletal malformations are easily detectable and, if found, should suggest further urological investigations. The embryological aspect of the association is explored. Two cases are presented and the relevant literature is reviewed.     

Cyst of seminal vesicle associated with ipsilateral renal agenesis

A case of cyst of seminal vesicle associated with ipsilateral renal agenesis in a twenty-three-year-old man presenting primarily with rectal symptoms is reported. The usual symptoms had been urinary bladder irritation and pain on ejaculation. The embryologic development of this rare entity is discussed.     

Vesicoureteral junction obstruction associated with unilateral renal agenesis

A 7-month-old boy with a solitary kidney showed recurrent urinary tract infection. Magnetic resonance urography helps in the identification of vesicoureteral junction obstruction associated with unilateral renal agenesis.