腹膜后巨大淋巴结增生症1例

患者男,39岁.体检时发现盆腔部腹膜后有一包块.CT检查提示:盆腔内腹膜后软组织肿块并点状钙化,血供丰富,考虑恶性肿瘤.患者自觉无明显不适,仅体重下降3 kg.体查:体温36.7℃,脉搏84次/min,呼吸18次/min,血压142/91 mmHg(1 mmFIg=0.133 kPa),腹部稍膨隆,无腹壁静脉曲张,未见胃肠型及蠕动波,全腹软,无压痛、反跳痛,下腹部触诊略硬,肿物触诊边界不清,无触痛,活动度差,未触及波动感及搏动感.肝、脾肋下未触及,无移动性浊音,肠鸣音正常.直肠指诊检查:无阳性发现.入院后行常规检查及肿瘤标记物检查均未见异常.并行腹膜后肿瘤切除术.术中见肿瘤位于盆腔腹膜后,左右髂血管交叉处,与周围血管及肠管无明显侵犯.     

胸内巨淋巴结增生症15例

胸内巨淋巴结增生症１５例庞其清胸内巨淋巴结增生症少见。１９６５年以来，我们经手术治疗１５例，效果良好。现报道如下：临床资料本组１５例中男８例，女７例。年龄１５～４４岁。临床症状以低热、胸痛、血沉加快和贫血为特征，本组有１例血红蛋白仅７ｇ／Ｌ、１例血沉...     

腹膜后局限性Castleman病(附3例报告)

目的提高腹膜后局限性Castleman病的诊治水平。方法回顾性分析3例腹膜后局限性Castleman病患者的临床资料,并进行文献复习。其中男2例,女1例,发病年龄49~61岁,中位年龄56岁,肿瘤位于腹膜后,大小3.0cm×3.5cm×4.0cm~4.0cm×4.5cm×6.0cm。结果 3例患者肿瘤均经手术成功切除并经术后病理证实,临床分类均属于局限型。术后随访6~12个月,未见肿瘤复发。结论腹膜后Castleman病临床少见,可发生于淋巴组织的任何部位,术前CT检查对诊断该病有一定帮助,确诊有赖于病理学检查,手术切除为首选治疗方法 。     

巨淋巴结增生症的临床特点及外科治疗

目的 探讨巨淋巴结增生症(castleman's disease,CD)的临床特点及外科治疗方法. 方法 分析2005年10月至2010年3月首都医科大学附属北京友谊医院收治9例巨淋巴结增生症患者的临床资料,其中男7例、女2例,平均年龄51.8岁.出现临床症状2例,包括咳嗽、胸闷、发热、乏力、盗汗等,其他为体检发现.9例患者术前均行胸部X线片、胸部CT、单光子发射计算机断层成像术(SPECT)和腹部B超检查.接受手术切除治疗. 结果 在临床分型中,单中心型CD 5例,多中心型CD 4例；病理分型中,透明血管型6例,浆细胞型1例,混合型2例.由于瘤体血供丰富,术中出血较多,平均出血量514.4ml,最多2 500ml.5例单中心型CD患者均生存,无复发；多中心型CD 4例,随访3～5年,4例均生存,其中2例分别于术后1年、3年后复发,再次行手术切除,术后病理结果与第1次手术相同. 结论 CD的诊断主要依靠影像及病理学,而最后确诊还应以病理学为准.无论哪种类型的CD外科切除均为有效的治疗方法,单中心型CD手术切除病变可达到彻底治愈的目的,而多中心型CD手术切除后仍有复发可能,应适当联合化疗、放疗等其他治疗手段.     

肾上腺区巨大淋巴结增生症l例报道并文献复习

巨大淋巴结增生症又称Castleman's Disease或血管滤泡性淋巴组织增生,1954年由Castleman首先报道.临床较少见,文献报道好发生于胸部纵膈,发生于腹膜后则极为少见.现报道1例腹腔镜微创手术治疗腹膜后局灶型巨大淋巴结增生症,并复习相关文献以加深对该病的认识,提高诊出率.     

巨淋巴结增生症临床分析

目的：提高巨淋巴结增生症的认识水平。方法：通过２例经手术及病理证实的巨淋巴结增生症的病例分析,结合文献复习,对本病的病因、临床表现、病理、诊断与鉴别诊断、治疗及预后进行讨论。结果：巨淋巴结增生症是一种异源性的罕见的淋巴组织增生性良性疾病。其组织形态上可分为透明血管型和浆细胞型两类,前者常表现为纵隔病变,后者好发于肠系膜和腹膜后淋巴结。结论：该病为少见病,病因尚不明确,患者多无病状,首选治疗为手术切     

巨大淋巴结增生症伴发肾损害二例

巨大淋巴结增生症（giantlymphnodehyperplasia,GLNH）是淋巴组织的一种慢性增生性疾病。由此病继发的肾脏损害国内尚无报道,近年我院收治2例,现介绍如下。例一女,15岁。1994年1月出现上腹绞痛伴黑便,胃镜诊断“十二指肠球部及降部出血坏死性炎症”,予禁食、抑酸等处理症状消失。此后双下肢曾两次出现暗红色丘疹,经“抗过敏”皮疹消退。3月底开始持续发热,最高体温38.5℃,伴尿泡沫增多,当时血WBC9．3×109／L,尿蛋白＋～＋＋,试验性抗涛治疗1个月,效果差,于1994年7月入我院。入院查体T37．4℃,贫血貌,肝右锁骨中线胁下20…     

腋窝Castleman'病彩色多普勒表现报告1例

1临床资料患者女,34岁。因发现左腋窝肿物2年余,于2007年5月30日入院。2年来患者自觉病灶逐渐增大,无不适。入     

Castleman's disease: a case report

Castlemans disease (CD) was described from Benjamin Castleman in 1954. The disease today is enumerated among lymphoproliferative disorders and has unknown etiology, but a interleukin-6 (IL-6) dysregulation and a reaction to viral antigens (HHV8) especially in patients with immunodeficiency is suspected. It is observed in adult and young people, in male or female with equal frequency; the appearance in childhood is extremely rare. The disease shows various clinical and histological pictures, with a localized type (involvement of one lymph node group) described more frequently than the multicentric one. Histological examination distinguish a "hyaline-vascular type" that represents approximately the 91%, a plasma cell type" that represents approximately the 9% has an aggressive clinical outcome, and the "mixed types". Initial symptoms are nearly absent, but not for the plasma cell type. We describe the clinical case of a female patient 21 years old. She reached our observation in May 1999, referring us for pelvic pains and amenorrhoea from four years. During 1996 she underwent to a laparoscopy that diagnosed an endometrial cyst on left ovary. A year later a new retroperitoneal mass was discovered and a second laparoscopy was performed with a little partial excision of the tumor. In our Institute the us and the TC showed a retroperitoneal mass of 4.5 cm of diameter, next to the uterus and the iliac left vessels. The patient underwent surgical laparotomic excision and histological examination showed hyaline vascular type of CD. Three years after surgery the patient is still free of any symptoms.     

Preiser's disease: a case report

Preiser's disease, or avascular necrosis of the scaphoid, is an exceedingly rare although debilitating pathologic process. A case of progressive avascular necrosis of the carpal scaphoid is presented together with a review of the possible etiology of this rare syndrome. Histologic evaluations of resected specimens have demonstrated a localized sequestrum of necrotic bone, leading to the belief that disruption of blood supply is a major predisposing factor. The diagnosis of Preiser's disease or avascular necrosis of the carpal scaphoid should be exclusively reserved to those cases that demonstrate a progressive clinical and radiographic sequence of osteosclerosis and subsequent fragmentation of the scaphoid.     

Friedrich's disease: a case report.

An eight-year-old girl was presented with painful swelling of the sternoclavicular joint. Radiological and scintigraphic examinations lead to a diagnosis of Friedrich's disease, aseptic necrosis of the sternal end of the clavicle. It is a rare condition which is to be differentiated from osteomyelitis, arthritis, or tumor. Because it is a self-resolving, benign condition, awareness of this disease will save the patient from unnecessary surgery.     

Castleman disease: a clinical case report

Castleman's disease is an enigmatic lymphoid disease of unknown etiology and has different clinical manifestations. The authors present a case of a young woman with cervical localization of Castleman disease, asymptomatic. The disease was misdiagnosed and was treated for five years as thyroiditis, diagnosis confirmed by ultrasonography, scintigraphy and cytology. The particular size of the neoformation and its constant growth leaded the authors to the surgical treatment. The thyroid was normal both macroscopically and with biopsy. The neoformation was 10 cm of diameter and covered the left side of the thyroid.     

Perianal Paget's disease: a case report

A case of perianal Paget's disease is presented. The salient features of this disease include perianal irritation, a perianal rash, and usually, as in this patient, an associated underlying carcinoma. The disease is rare and has to be differentiated from malignant melanoma, Bowen's disease and transitional cell carcinoma. This patient was also remarkable since the associated malignancy was an equally rare carcinoma of anal gland origin.     

Disseminated Kikuchi-Fujimoto disease: a case report

Subacute necrotizing lymphadenitis or Kikuchi-Fujimoto disease is a benign pathological entity diagnosed chiefly in young adults. We report a case in a 20-year-old woman who presented with swollen lymph nodes and a fever. Disseminated lymphadenopathy with nodes measuring up to 6 cm in diameter was found upon physical examination. The erythrocyte sedimentation rate was elevated to 40 mm/h and the lactic dehydrogenase level to 593 IU/l. Findings were negative from serological tests for rubella, hepatitis B, hepatitis C, HIV, and toxoplasmosis, as well as from tests for tuberculosis. A biopsy of a cervical lymph node showed nonsuppurative necrosis, karyorrhexis, and a marked histiocytic reaction consistent with Kikuchi-Fujimoto disease. No treatment was given, and a full recovery was achieved within 3 months. In this patient, the disseminated lymphadenopathy and constitutional symptoms strongly suggested a hematological malignancy and more specifically a lymphoproliferative disease.     

脊柱包虫病1例报道

脊柱包虫病是一种罕见疾病,在畜牧地区相对多见,发病隐匿,临床表现及影像学表现不典型,难以早期确诊,易误诊为结核、肿瘤等,从而延误治疗。我科收治1例脊柱包虫病患者,术前误诊为结核,报道如下。