颅面骨纤维异常增殖症的CT诊断

目的:探讨颅面骨纤维异常增殖症的CT诊断价值.方法:回顾性分析12例经手术病理证实的颅面骨纤维异常增殖症的CT表现.结果:单骨型7例,多骨型5例,磨砂玻璃状改变7例,丝瓜瓤状改变2例,囊性改变1例,混合性密度增高1例,象牙骨质改变1例.结论:CT扫描能准确显示颅面骨纤维异常增殖症的形态、部位、范围,有助于定位、定性诊断,为临床治疗方案的制定提供依据.     

颅面骨骨纤维异常增殖的CT影像诊断

目的：探讨ＣＴ面面 骨骨纤维增生殖症的诊断价值。方法：回顾性分析我院１９９０年至今１３例颅面骨骨纤维异常增殖症的ＣＴ表现。结果：ＣＴ表现为三型：硬化型、囊肿型、混合型。结论：ＣＴ对颅面骨骨纤维异常增殖症的诊断具有重要参考价值。     

颅面骨骨纤维异常增殖症的CT影像诊断

目的:探讨颅面骨骨纤维异常增殖症的CT影像特点,提高其诊断精确性。方法:回顾性分析23例经手术或活检病理证实的骨纤维异常增殖症的临床、病理及影像特点。结果:单骨型6例(26.1%),多骨型17例(73.9%);绝大多数骨纤维异常增殖症的影像表现为多形态改变,主要包括:磨玻璃样增白伴膨胀改变;膨胀囊状改变伴磨玻璃样密度;仅2例表现为弥漫性硬化改变。其中合并病理性骨折1例,Albfight综合征1例。正确诊断21例(91.3%),误诊2例。结论:颅面骨骨纤维异常增殖症的影像表现有一定特征性,CT检查对其诊断、鉴别诊断及指导治疗具有重要意义。     

颅面骨纤维异常增殖症13例临床分析

目的：研究颅面骨纤维异常增殖症（Ｆｉｂｒｏｕｓｄｙｓｐｌａｓｉａ）的诊断及治疗,复发和恶变。方法：总结１３例颅面骨ＦＤ的临床资料并结合文献分析。结果：１３例颅面骨ＦＤ临床表现为无痛性渐进肿块,ｘａｙ表现有毛玻璃型和硬化型。治疗以手术切除病灶,改善畸型和功能障碍,１３例中复发３例,恶变２例。结论：颅面骨ＦＤ诊断应临床、影像学、病理相结合。治疗以保守性手术为主。ＦＤ可复发和恶变,放疗无助于预防复发,反而刺激恶变。     

颅面骨纤维异常增殖症18例分析

报告颅面骨骨纤维异常增殖症１８例，手术治疗１７例，手术进路：经唇龈沟切口１１例，侧鼻切开５例，左耳后切口１例，术中削除或部分削除增殖的病变骨质，术后随地年至１８年，效果良好，无复发。结合病史及Ｘ线表现本病不难诊断，确诊靠病理，需与骨化纤维瘤等疾病鉴别。     

颅面骨骨纤维异常增殖症18例

介绍颅面骨骨纤维异常增殖症18例,随访0.5～0.8年经手术治疗的17例,均良好,无复发.手术进路经唇龈沟切口11例,侧鼻切开5例,左耳后切口1例,削除增殖的病变骨组织.认为本病结合病史及X线表现不难诊断,靠病理确诊.需与骨化纤维瘤等病鉴别.手术不必过于强求完全切除病骨,以修面容为目的,以免切除过多造成面部医源性畸形.本病预后良好.先天性骨骼中胚叶发育异常可能是本病的致病原因,有待进一步研究.     

颅面骨骨纤维异常增殖症——附17例报告

颅面骨骨纤维异常增殖症──附１７例报告第二军医大学长征医院耳鼻咽喉科彭玉成，陆书昌，郗向红我院１９７５～１９９４年经手术治疗颅面骨骨纤维异常增殖症患者１７例，术后均经病理证实，现报告如下。临床资料一、一般情况１７例中，男６例，女１１例，男女之比约为１...     

颅面部骨纤维异常增殖症的CT诊断

目的 评价CT对颅面部骨纤维异常增殖症的诊断价值。方法 回顾性分析资料完整的18例颅面部骨纤维异常增殖症CT扫描图像。2例行螺旋CT扫描薄层及三维重建；2例行HRCT横轴位扫描；其余行常规CT扫描。结果 14例累及多个颅面骨；单骨受累4例(右侧颞骨2例；左侧上颌骨、蝶骨各1例)。CT示受累颅面骨弥漫性膨大、畸形，骨皮质变薄，病骨密度改变主要有3种：磨玻璃样变；囊状低密度区；硬化区。3种密度可以混和存在。根据病变的密度分为3种类型：①硬化型8例；②变形性骨炎型8例；③囊型2例。同时伴随病变区内或邻近的自然腔隙、孔道、窦、管变形狭窄或闭塞。结论 CT扫描可清楚显示颅面部骨纤维异常增殖症骨质改变、病变范围及伴随表现，对本病的诊断、治疗及随访起重要作用。     

颅面骨骨纤维异常增殖症的CT诊断

目的对颅面骨的骨纤维异常增殖症的CT诊断进行讨论和研究。方法对CT诊断为骨纤维异常增殖症,并经手术和病理证实的30例,对其CT表现进行了分析对照和研究。结果30例中,29例为多发,仅1例为单发,其中囊样型3例、硬化型16例、混合型11例。结论CT检查能准确的显示病变部位和范围。     

颅面骨纤维异常增殖症与骨化纤维瘤鉴别的研究进展

纤维骨性病变（fibro—ossous lesions，FOLs）是一组正常骨含有各种骨化成分的纤维组织取代的疾病，包括发育和反应性或异常增殖病变以及肿物。FOLs70％以上发生于头颈部，下颌多于上颌。根据2005年WHO分类，包括三种病变，即纤维异常增殖症（fibrous dysplasia，FD）、骨异常增殖症（osseous dysplasia，OD）和骨化纤维瘤（ossifying fibroma，OF）。这三类疾病的临床、X线和组织病理学，都有许多相似、交叉与重叠，因此鉴别困难。本文就FD与OF鉴别进行文献复习。     

骨纤维异常增殖症的X线与CT表现

目的:提高X线与CT检查对骨纤维异常增殖症(fibrous dysplasia of bone,FDB)的认识,探讨其影像学表现与病理之间的关系。方法:回顾分析17例由手术病理证实的FDB的X线与CT表现。结果:由于病理上骨组织成分的不同,FDB在X线片和CT上表现为皮质变薄,呈膨胀性骨质破坏,无骨膜反应及软组织肿块5例;髓腔呈磨玻璃样密度改变3例;骨干增粗、变形,髓腔呈丝瓜肉样改变4例;虫蚀样改变1例,骨质广泛增生改变2例;有上述两种或两种以上改变2例。结论:大多FDB具有较典型的影像学表现,X线片大多可显示病变的整体观及病变特点,但CT可通过横断面及多平面图像重组来显示病变的内部结构、比邻关系、范围,同时可测量CT值,尤其在解剖结构复杂的部位更具优势,可作为首选检查。     

1例颅面骨纤维异常增生症行内窥镜下视神经减压术的护理

总结1例颅面骨纤维异常增生症患儿在鼻内窥下行视神经减压术的护理方法 ,该手术解剖结构复杂,凶险大,通过细心的术前准备及术后护理,患儿康复出院。     

Unusual manifestations of craniofacial fibrous dysplasia: clinical, endocrinological and computed tomographic features.

Clinical, endocrinological and computed tomographic features of three patients with unusual manifestations or complications of craniofacial involvement of fibrous dysplasia are presented. One patient with polyostotic fibrous dysplasia presented in late pregnancy with acute onset of bilateral optic nerve compression and blindness secondary to a rapidly expanding mass of fibrous dysplasia tissue involving the sphenoid, pituitary and optic chiasm regions. A second patient with polyostotic fibrous dysplasia developed thyrotoxicosis and probable gigantism/acromegaly in keeping with a rare form of McCune-Albright syndrome. Extensive bony distortion of the skull and facial bones by fibrous dysplasia made clinical recognition of these complications more difficult. A third patient had monostotic fibrous dysplasia with marked sclerosis of the sphenoid bone on plain radiographs which mimicked appearances of a meningioma and resulted in a negative craniotomy as computed tomography was not yet available at the time of presentation. Each case demonstrated rare complications of craniofacial fibrous dysplasia and highlighted the wide spectrum of appearances in which it may manifest, often resulting in overlap and diagnostic confusion with other disease processes. The value of computed tomography in assessment is emphasized.     

骨纤维异常增殖症的X线诊断及价值

目的：分析骨纤维异常增殖症的临床特点和X线表现,探讨X线对骨纤维异常增殖症的诊断价值。方法：收集46例经手术病理证实的骨纤维异常增殖症的X线表现特征。结果：X线表现较复杂,特征性表现主要为毛玻璃样改变、囊状低密度影和斑块样硬化,无明显骨膜反应存在。结论：X线仍是诊断骨纤维异常增殖症的良好方法,CT和MRI对判断周围组织变化有帮助。     

小脑肿瘤的CT和MRI诊断

目的分析小脑肿瘤的CT和MRI影像特征。方法对31例经病理证实的小脑肿瘤CT和MRI表现进行回顾性分析和总结。结果 31例中髓母细胞瘤9例,血管母细胞瘤8例,星形细胞瘤6例,转移瘤4例,室管膜瘤2例,脉络丛乳头状瘤1例,蛛网膜囊肿1例。结论 CT与MRI各有特点、优势互补,可以明显提高小脑肿瘤的正确诊断率。     

Imaging Diagnosis of Monostotic Fibrous Dysplasia in Thoracic and Lumbar Spine Vertebrae

The X-ray radiograph, CT scan and MRI appearance of 5 patients with pathologically proven fibrous dysplasia in thoracic and lumbar spine vertebrae were retrospectively analyzed. Plain radiographs, CT scans and MR images showed the presentation of eccentric lesion with intact cortex bone and marginal sclerosis in vertebral bodies without involvement of vertebral appendix and ex- traosseous soft tissue. The lesion masses were round （one being oval-shaped） and radiolucent in plain radiographs and CT scans. Homogeneous long signal was observed on Tl weighted image and strongly enhanced when gadolinium was administered. On T2 weighted MRI, short signal was found in the anterior part of the mass, long signal in the posterior part, and short and slight long signal in the middle part, without partitioning and laminating change. There was a good correlation between radiological features and surgical findings. These findings may be useful to diagnose fibrous dysplasia m spree.     

Imaging diagnosis of monostotic fibrous dysplasia in thoracic and lumbar spine vertebrae

Summary The X-ray radiograph, CT scan and MRI appearance of 5 patients with pathologically proven fibrous dysplasia in thoracic and lumbar spine vertebrae were retrospectively analyzed. Plain radiographs, CT scans and MR images showed the presentation of eccentric lesion with intact cortex bone and marginal sclerosis in vertebral bodies without involvement of vertebral appendix and extraosseous soft tissue. The lesion masses were round (one being oval-shaped) and radiolucent in plain radiographs and CT scans. Homogeneous long signal was observed on T1 weighted image and strongly enhanced when gadolinium was administered. On T2 weighted MRI, short signal was found in the anterior part of the mass, long signal in the posterior part, and short and slight long signal in the middle part, without partitioning and laminating change. There was a good correlation between radiological features and surgical findings. These findings may be useful to diagnose fibrous dysplasia in spine.     

纤维性骨皮质缺损的MRI诊断与鉴别诊断

目的探讨纤维性骨皮质缺损的MRI表现及其鉴别诊断。方法对32例经随访观察1～4年（26例）、临床病理证实（6例）的纤维性骨皮质缺损患者的临床资料及MRI表现进行分析,并加以鉴别诊断。结果 32例纤维性骨皮质缺损中,位于股骨远侧干骺端16例,股骨骨干下段3例,股骨近侧干骺端3例,胫骨近侧干骺端8例,胫骨骨干上段2例;右侧17例,左侧15例;且病灶大多位于病骨后侧份,内侧份皮质区;病灶大多呈类圆形、椭圆形,边界清楚,周围未见骨膜反应及软组织肿胀,病灶大小约0.5～2.6cm,多呈稍长T1稍长T2、稍短T2信号,并周围见低信号线样改变,11例增强扫描均有不同程度强化,多为轻～中度。14例经随访观察,其中7例病灶无改变,5例病灶稍有缩小,2例发展为非骨化性纤维瘤。结论纤维骨皮质缺损的MRI表现有一定的特征性,有助于该病的诊断,并能进行鉴别诊断。