成人乳头状淋巴管内血管内皮细胞瘤1例报道

乳头状淋巴管内血管内皮细胞瘤(Papillary intralymphatic angioendothelioma,PILA)好发于婴幼儿和儿童,成人罕见。现报道1例并综合国内外文献,进行讨论。1材料与方法1.1临床资料患者女性,26岁。因下唇黏膜隆起数年,近1年增大明显入院。病变无疼痛、破溃,     

血管内乳头状内皮细胞增生的超声表现及误诊分析

目的 分析血管内乳头状内皮细胞增生(IPEH)的超声表现及误诊原因,以提高超声医生对本病的认识.方法 回顾性分析2010年6月—2019年11月经手术活组织病理检查证实的26例IPEH超声误诊病例资料.结果 本组误诊率为100％,8例既往下肢深静脉血栓患者、4例肾衰竭透析患者及2例糖尿病患者,随诊既往疾病时发现肢体皮下...     

血管内乳头状内皮增生的高频超声表现

目的 探讨血管内乳头状内皮增生(IPEH)的高频超声(包括二维及彩色多普勒血流)成像特征,帮助该病的诊断及鉴别诊断.方法 收集2014年1月至2019年11月于南京医科大学第一附属医院经穿刺或手术病理证实的IPEH患者21例,回顾性分析患者的年龄、性别和临床病史.其中8例患者(年龄17～63岁,平均44.8岁,女性4例...     

乳腺乳头状淋巴管内血管内皮细胞瘤临床病理特征分析

目的探讨乳腺乳头状淋巴管内血管内皮细胞瘤(PILA)的临床病理特征、免疫表型、诊断与鉴别诊断及预后。方法对1例乳腺PILA行HE及免疫组化染色观察,并进行随访及文献复习。结果该病主要病理改变为薄壁囊状扩张的大小不等血管腔隙,腔内衬覆内皮细胞及鞋钉样瘤细胞。管腔内瘤细胞排列呈乳头状皱褶和玻璃样变轴心。免疫组化显示肿瘤细胞CD34、CD31、vimentin和bcl-2(+)。随访6年无复发、转移,预后良好。结论乳腺PILA是一种非常罕见的交界性血管性肿瘤,组织学形态易与多种良性、恶性血管性肿瘤混淆。经扩大手术切除后预后良好。     

原发性脾脏血管肉瘤1例

病例女,52岁。因B超体检发现多发低回声脾脏占位,而到我院就诊,病程中无腹痛、发热等症状,已绝经。查体：腹部平软,全腹无压痛,未扪及包块,肝脾未触及,无叩痛。血常规和尿常规正常。CT检查所见：脾脏增大,实质内见     

多发性恶性血管内乳头状血管内皮瘤1例

患者女性，51岁。因反复双下肢及腰腹部多发性肿块伴疼痛5年余，加重7个月人院。患者既往4次因右大腿和胭窝“血管瘤”手术治疗。最初病变发生于右大腿后部皮下软组织，为单发，以后在原处复发4次，腰背部、腹壁、双下肢也先后出现类似肿块。无外伤史。查体：腰部、右胭窝及两小腿腓肠肌中部多个直径2cm肿块，无红肿。共切除病灶6     

脾脏梭形细胞血管内皮细胞瘤的CT和MRI表现1例

脾脏除淋巴瘤之外的原发性肿瘤并不多见,其中最常见的是血管瘤和血管肉瘤,而血管内皮细胞瘤则非常罕见,国内尚未见报道。我院遇经病理证实的原发于脾脏的梭形细胞     

血管内乳头状内皮细胞增生1例

正患者男性,32岁。因发现左足跟包块伴间断性疼痛2月入院。查体:左足跟见一大小约2 cm×2 cm的近圆形隆起,表面皮肤粗糙,黄褐色,肿块边界较清,质地较硬,活动度差,无压痛。病理检查巨检:带梭形皮瓣的不整形软组织1块,大小3 cm×2 cm×2 cm, 皮肤面积3 cm×2 cm, 切面灰白间灰红色,质地较硬。镜检:皮肤组织鳞状上皮角化过度,真皮层内见畸形扩张的血管,血管腔内血栓形成并机化(图1),     

后纵隔卡波西样血管内皮细胞瘤1例

患者女,35岁.2年前无明显诱因出现后背疼痛,间断性酸胀痛.查体发现左侧颈椎C4～6椎旁压痛,T6、7棘间压痛,无叩击痛.尿白细胞计数113/μl,上皮细胞计数244/μl,细菌计数14010.5/μl,潜血(+++).胸部CT增强扫描:于主动脉弓水平、左后纵隔、食管左后方与T4椎体间见一团状软组织密度病变,与周围分界清晰,呈不均匀强化,部分强化区域CT值达200 HU(图1A).MRI:T4椎体左侧类圆形混杂信号肿块,中心星短T1稍长T2信号,其内夹杂点片状长T2信号,病灶边缘星长T1等T2信号(图1B～D).考虑神经源性肿瘤可能.     

Sonographic features of intravascular papillary endothelial hyperplasia (Masson's tumor) in the forearm

Intravascular papillary endothelial hyperplasia, also known as Masson's tumor, is a benign, vascular lesion in which there is papillary proliferation of endothelial cells. The lesion presents as a palpable soft-tissue mass, often located within normal or dilated vascular spaces, and may be mistaken for a sarcomatous tumor on imaging. We present the case of an intravascular papillary endothelial hyperplasia in the forearm, with a remarkable appearance on color Doppler sonography, and suggest that this entity will be encountered more frequently by sonologists in the future.     

Intravascular papillary endothelial hyperplasia as a rare cause of cervicothoracic spinal cord compression: A case report

BACKGROUNDIntravascular papillary endothelial hyperplasia (IPEH) is a rare benign reactive vascular lesion that grows into an expansile compressing mass. It most commonly involves the skin and subcutaneous tissue. Spinal involvement is rare, with only 11 reported cases in the literature. We report, to our knowledge, the first case of IPEH in the cervicothoracic spinal canal and present a literature review.CASE SUMMARYA 27-year-old man presented with acute-onset neck pain, numbness, and weakness in his extremities. Magnetic resonance imaging showed an epidural mass in the cervicothoracic (C6-T1) spinal canal and vertebral hemangioma (VH) involving the C7 vertebral body. C6-T1 Laminectomy and radical excision of the mass were performed. Histopathological examinations revealed papillary proliferation of vascular endothelial cells with thrombus formation, and an IPEH diagnosis was made. By his 6-mo follow-up appointment, his symptoms were relieved without recurrence. The possible pathogenesis, clinical and imaging features, differential diagnosis, and management of IPEH were reviewed.CONCLUSIONWe report, to our knowledge, the first case of IPEH in the cervicothoracic spinal canal, treated via complete resection, and showing a favorable outcome. We found a causal relationship between spinal IPEH and VH; this partly explains the mechanism of IPEH.     

乳头状肾细胞癌1例

患者男,58岁,无明显诱因出现腹胀,饭后加重伴胸闷2个月;既往体健.查体:左中腹扪及约10 cm×8cm肿物,触之质硬,固定,边界尚清,有压痛并向会阴部放射.实验室检查未见明显异常.腹部MRI:左肾弥漫性增大,约15.2 cm×8.7 cm×7.0 cm,信号不均,肾门区软组织信号增多(图1A),脂肪抑制T2WI示弥漫...     

乳腺假血管瘤样间质增生MRI表现1例

患者女,36岁,发现左乳肿物半年,逐渐增大2个月入院。查体:左乳外下象限触及一大小约6.0cm×4.0cm肿物,质硬,边界清,活动度可,表面皮肤光滑,未见"橘皮样"改变。超声:左乳囊实性占位,BI-RADS 3类。乳腺MRI:左乳外下象限团块,边界清楚,约6.8cm×6.0cm×5.5cm,FSPGR呈等信号,内见裂隙样低信号区(图1A);脂肪抑制T2WI上呈结节状、片状稍高信号,内见裂隙样高信号