Progressive diaphyseal dysplasia (Engelmann disease(: scintigraphic- radiographic-clinical correlations

Four patients (2 males, 2 females; ages 15-47 yrs.) with variable clinical, radiographic, and scintigraphic manifestations of progressive diaphyseal dysplasia (PDD) or Engelmann disease were studied with 99mTc methylene diphosphonate bone imaging and radiographic skeletal surveys. Comparison of the results of the two imaging procedures showed that some affected bones were scintigraphically normal but radiographically abnormal and vice versa. These findings suggest that the lesions of PDD may mature, causing a significant decrease in disease activity, and that abnormally increased radiopharmaceutical accumulation during bone scintigraphy appears to be a sensitive indicator of disease activity.     

新生儿和婴儿正常脑发育的MRI研究I．关于髓鞘形成

目的：通过本研究建立中国婴儿正常脑髓鞘化的时间表。材料与方法：选１００例２岁以内的没有神经系统疾病的小儿，按月龄分成５组，用０．３５ＴＭＲ仪在Ｔ１加权像（Ｔ１ＷＩ）和Ｔ２加权像（Ｔ２ＷＩ）上分别观察髓鞘形成的进程及在Ｔ２ＷＩ上对灰白质分辨进行分期。结果：（１）灰白质分辨分为５期，新生儿１００％属Ⅰ期，６个月内的婴儿８８％为Ⅱ期，６个月以上的婴儿２０％为Ⅲ期、８０％为Ⅳ期，１４个月时达Ⅴ期，１８个月时接近成人。（２）髓鞘化时间，后颅窝结构３～４个月时即达成人早期，内囊后肢在６个月内、前肢在７～１０个月，胼胝体压部是４个月、膝部是６个月，顶枕叶１０个月，额叶１２个月，颞叶１５～１８个月，皮层下的白质持续到２岁以后。结论：脑灰白质分辨的５期，反映了脑发育的过程，与月龄关系密切，对判断脑发育是否落后非常重要     

Optimizing joint-imaging: (CT)-arthrography

The technique of CT arthrography and arthrotomography of the major joints is discussed. Also, the types of contrast media, double or single contrast technique, film-screen combinations, injection techniques and additional pain testing are discussed.Correspondence to: J. Freyschmidt     

Pericardial effusions (85 cases): radiological aspects (author's transl)]

A radiological study of 85 patients with acute pericarditis and effusion included a group of 35 cases observed before the introduction of ultrasonography and a second group of 50 patients in whom the presence of pericarditis had been confirmed by this investigation. The most important conclusions established were the following: --Absence of radiological signs in 55% of cases (group 1 : 46%, group 2 : 60%); normal heart size in 54% (group 1) and 78% (group 2), and increased size in 34% (group 1) and 20% (group 2). --Hilar manifestations (overlapping and obscuring of the left hilar region) in 26% of cases with a clear predominence of the left forms (14 out of 22). The cardiomegaly was not significant in 28% (group 1) and 14% (group 2). --The high frequency of pericarditis with a normal heart size has to be emphasized. The diagnostic value of hilar manifestations is also mentioned; the sign of left hilar overlapping is described in greater detail. --An overall comparison between the two groups shows, more particularly, the equal importance of left hilar manifestations for the radiological diagnosis of pericarditis. In a general way, it would appear that these hilar signs are the only elements which enable objective diagnosis of pericardial effusions on standard films.     

Lymphangioleiomyomatosis: solitary abdominal manifestation (2009: 9b)

Lymphangioleiomyomatosis (LAM) is a rare disease that usually affects premenopausal woman and is characterized by cystic lung lesions and lymphatic disorders. We report a case of a 23-year-old woman who presented with diffuse, but increasing abdominal pain. Transabdominal ultrasound showed multiple cystic formations. Due to the patient’s uncharacteristic symptoms, an exploratory laparotomy with tissue sampling was performed, and the diagnosis of LAM was confirmed by two independent pathologists. With computed tomography a broad abdominal, but no pulmonary, manifestation could be established. During sirolimus therapy the patient showed clinical benefit, but only slight progress in computed tomography.     

Galaktose-1-Phosphat-Uridyl-Transferase (EC: 2.7.7.11): Elektrophoretische Darstellung

Zusammenfassung Die elektrophoretische Darstellung der Uridyltransferase aus Erythrocyten durch horizontale Stärkegelelektrophorese und Formazanreaktion wird beschrieben.

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Summary The demonstration of red cell galactose-1-phosphate-uridyl transferase by means of horizontal starch gel electrophoresis and tetrazolium staining is described.

Mit Unterstützung durch die Deutsche Forschungsgemeinschaft.     

Erratum: Radiologe (1997) 37: 802–806

Ohne Zusammenfassung     

Erratum: Radiologe (1998) 38:614–623

Ohne Zusammenfassung