Heart failure due to severe supravalvular aortic stenosis in painless type A aortic dissection

Severe supravalvular aortic stenosis is a rare complication of aortic dissection. Painless aortic dissection is also relatively rare. We report the case of a 67-year-old man who had New York Heart Association class III heart failure without chest pain and was found to have supravalvular aortic stenosis secondary to chronic type A aortic dissection. The patient underwent ascending aorta and hemiarch replacement with selective antegrade cerebral perfusion under deep hypothermic circulatory arrest. The patient was discharged to home with complete resolution of heart failure and has been carefully followed up for 1 year, during which he has experienced no symptoms.     

Aortic cannulation through the aneurysm for repair of thoracoabdominal aortic aneurysms

We hereby present our experiences with arterial cannulation through the aneurysm in patients with thoracoabdominal aortic aneurysm. This can be a good option for thoracoabdominal aortic aneurysm repair in patients with diseased peripheral arteries.     

Aortic cusp extension valvuloplasty for rheumatic aortic valve disease: midterm results

BACKGROUND: The introduction of composite graft repair of aortic root aneurysm by Hugh Bentall in 1968 promised Marfan patients the choice for a normal life expectancy. We performed our first Bentall composite graft procedure in 1976 and herein report our 24-year experience with 271 Marfan patients. METHODS: Between September 1976 and August 2000, 232 Marfan patients had a composite graft replacement of the aortic root, 15 patients received a homograft, and 24 had a valve-sparing procedure. RESULTS: Two hundred thirty-five Marfan patients underwent elective aortic root replacement with no 30-day mortality. Two early deaths occurred among 36 patients who underwent urgent or emergent operation. Eighty-three percent of patients in this series are currently alive. The actuarial freedom from thromboembolism, endocarditis, and reoperation on the residual aorta 20 years postoperatively was 93%, 90%, and 74%. Twenty-four patients have undergone valve-sparing procedures with encouraging results. CONCLUSIONS: Elective aortic root replacement for Marfan patients can be performed with low operative risk. Elective repair before the aortic root reaches 6 cm in diameter is recommended to minimize risk of dissection and rupture.     

Giant aortic aneurysm 18 years after repair of double-outlet right ventricle with pulmonary stenosis

Substantial long-term morbidity after a successful operation in complex congenital heart defects is a matter of concern. We present a patient with a giant ascending aortic aneurysm 18 years after repair of a double-outlet right ventricle with pulmonary stenosis. Our report emphasizes the need for ongoing follow-up into adulthood.     

Aortic valve repair for aortic stenosis in adults

The stenotic aortic valve was surgically repaired in 48 adults, 21 women and 27 men, aged 38 to 83 years. Five had congenital aortic stenosis (AS), with a mean aortic valve gradient and area of 58 +/- 23 mm Hg (standard deviation) and 0.54 +/- 0.13 cm2, respectively; 32 had senile AS with a mean aortic valve gradient and area of 43 +/- 20 mm Hg and 0.98 +/- 0.41 cm2; and 11 had rheumatic AS with a mean aortic valve gradient and area of 59 +/- 24 mm Hg and 0.47 +/- 0.15 cm2. Only 6 patients underwent isolated aortic valvoplasty, 11 underwent concomitant mitral valve procedure, and 34 underwent concomitant coronary revascularization. Repair consisted of decalcification in 33 patients and decalcification as well as commissurotomy in 15 patients. There were three hospital deaths, none related to the aortic valve. Only 2 patients (both rheumatic) did not improve clinically. During follow-up (mean, 64 +/- 41 months) aortic valve restenosis developed in 24% (10 patients, 3/5 congenital, 4/11 rheumatic, and 3/32 senile) at a mean of 64 +/- 28 months. Postoperative Doppler echocardiographic assessment of 21 patients with senile AS at 1.1 +/- 2.7 and 18.1 +/- 1.4 months showed significantly lower aortic valve gradient and improved area in comparison with preoperative values. At 36 +/- 2.7 months, aortic valve gradient and area were not significantly different than preoperative values, and at 58.5 +/- 2.6 months aortic valve gradient was 1.41 (p = 0.07) times the preoperative value. At 7 years, actuarial freedom from aortic valve-related symptoms of the patients with senile AS was 87%. We conclude that in select patients aortic valve repair results in excellent relief of AS. Late restenosis is expected and more likely to occur in the valves with congenital and rheumatic disease than in those with senile disease.     

Aortic root surgery in Marfan syndrome: Comparison of aortic valve-sparing reimplantation versus composite grafting

OBJECTIVE: The objective of this study was to compare the results of aortic valve-sparing reimplantation and aortic root replacement with mechanical valve conduits in patients with Marfan syndrome undergoing operation for aortic root aneurysms.Patients and methods Between March 1979 and April 2002, 119 patients with clinical evidence of Marfan syndrome underwent composite graft replacement with mechanical valve conduits (n = 74) or aortic valve-sparing reimplantation according to David (n = 45). The underlying causes were aortic dissection type A (43 patients) and aneurysms (76 patients). RESULTS: Patients undergoing aortic valve reimplantation were younger compared with patients undergoing composite grafting (28 vs 35 years, P =.002) and had longer intraoperative aortic crossclamp times (125 vs 78 minutes, P <.0001) and extracorporeal circulation times (162 vs 124 minutes, P <.0001). Early postoperative mortality was 6.8% (n = 5) in patients undergoing composite grafting and 0% in patients undergoing aortic valve reimplantation (P =.15). Mean follow-up was 30 months for patients undergoing aortic valve reimplantation and 114 months for patients undergoing composite grafting. Freedom from reoperation and death after 5 years postoperatively was 92% and 89% in patients undergoing composite grafting and 84% and 96% in patients undergoing aortic valve reimplantation (P =.31; P =.54), respectively. Thromboembolic complications or late postoperative bleeding occurred in 17 patients undergoing composite grafting, and an early postoperative event occurred in 1 patient undergoing aortic valve reimplantation. CONCLUSIONS: The results of aortic valve reimplantation and composite grafting of the aortic valve and ascending aorta with mechanical valve conduits are similar with regard to early and mid-term postoperative mortality and to the incidence of late reoperations in patients with Marfan syndrome. The low risk of thromboembolic or bleeding complications favors aortic valve reimplantation in these patients.     

Aortic valvotomy in the treatment of congenital aortic stenosis

Forty patients aged 1.5-23 (mean 11) years underwent open aortic valvotomy for congenital aortic stenosis. Mean preoperative peak aortic gradient for the group was 88 (SD +/- 24) mmHg. Follow-up data was available on all patients for a total of 269 patient-years (means 6.6 year). There was no early mortality, and only one (2.5%) late death. During the follow-up period 3 patients (7.5%) required aortic valve replacement. Actuarial survival curves predict a 7 year survival of 95.7 (SE +/- 8.4%) for all patients, and a freedom from reoperation rate at 6 years of 8.7 (SE +/- 9.3)%. Symptomatic results in the survivors were excellent (97.5% NYHA Class I). Data from this series compares favourably with the literature which is reviewed for a total of 1136 patients undergoing open aortic valvotomy.     

Aortic dissection after aortic valve replacement in patients with valvular aortic stenosis

Aortic dissection occurred after aortic valve replacement in two patients with valvular aortic stenosis. Clinical and necropsy findings are described.