先天性大疱性表皮松解症新生儿的护理

目的总结先天性大疱性表皮松解症新生儿的护理。方法对28例先天性大疱性表皮松解症新生儿实施保护性隔离、皮肤护理、黏膜护理、建立静脉通道、营养支持、密切观察病情和心理护理等全面的护理措施。结果 28例先天性大疱性表皮松解症新生儿均好转出院。结论对先天性大疱性表皮松解症新生儿在治疗过程中积极预防感染,并采取有效的综合护理尤为重要。     

一例先天性对称性皮肤缺损症伴大疱性表皮松解症新生儿的护理

一例先天性对称性皮肤缺损症伴大疱性表皮松解症新生儿的护理孙美农，裴莲焕先天性皮肤缺损和先天性大疱性表皮松解症均为遗传性疾病。前者属新生儿的一种罕见的先天性皮肤异常，［１］又称皮肤发育不全。此病指出生时即有表皮和真皮，甚至皮下组织的先天性缺损，还可伴大...     

27例先天性肠旋转不良新生儿的围术期护理

[目的]总结先天性肠旋转不良新生儿的围术期护理。[方法]对27例先天性肠旋转不良新生儿行手术治疗,同时加强术前准备、维持水电解质平衡,术后密切观察患儿腹部体征,做好保暖、呼吸道护理、有效胃肠减压、合理营养支持和切口管理等。[结果]1例死亡,26例术后恢复良好,痊愈出院。[结论]加强先天性肠旋转不良新生儿的围术期护理是手术成功的保证。     

新生儿先天性大疱性表皮松解症的护理

目的：总结本院5例新生儿先天性大疱性表皮松解症的护理。方法：对5例足月新生儿进行观察护理。结果：经过精心观察护理及预防感染,5例新生儿均治愈出院。结论：本病缺乏满意的临床治疗方法,极大影响患儿生长发育,甚至危及生命,加强护理、预防感染是减少死亡的关键。     

10例新生儿先天性膈疝的围术期护理

[目的]探讨新生儿先天性膈疝的护理方法,提高抢救成功率及护理质量。[方法]回顾医院2016年1月—2018年1月收治的10例新生儿先天性膈疝的临床资料,总结新生儿先天性膈疝患儿的围术期护理方法。[结果]10例患儿1例死于呼吸循环衰竭,9例手术患儿术后病情逐渐稳定,痊愈出院。[结论]对新生儿先天性膈疝患儿积极改善肺功能,维持呼吸循环功能,及时手术治疗,术后行机械通气,加强呼吸道管理,能明显提高患儿抢救成功率。     

21例先天性唇腭裂新生儿的护理体会

[目的]总结先天性唇腭裂新生儿的护理体会。[方法]回顾性分析21例先天性唇腭裂新生儿的临床资料。[结果]本组21例先天性唇腭裂新生儿住院期间均未发生上呼吸道感染、新生儿肺炎、窒息等并发症,母乳喂养率95%。[结论]加强先天性唇腭裂新生儿的护理有利于预防并发症的发生。     

阴道成形术治疗先天性无阴道病人的围术期护理

[目的]总结先天性无阴道病人行乙状结肠代阴道术的围术护理。[方法]对16例先天性无阴道病人入院后进行了心理状态的评估,健康教育,术前皮肤肠道阴道及阴道模具的准备;术后进行了饮食指导、会阴部及各种引流管的护理、疼痛护理和人工阴道模具的置放及护理;出院时的康复护理、健康宣教等措施。[结果]16例病人均痊愈出院,无一例发生并发症。[结论]加强先天性无阴道病人行乙状结肠代阴道术的围术护理是手术成功的保证。     

1例先天性大疱性表皮松解症伴贫血病人的护理

<正>先天性大疱性表皮松解症(epidermolysis bullosa,EB)是一组以皮肤脆性增加、轻微摩擦或外伤即可导致皮肤或黏膜水疱、血疱、糜烂为共同特点的遗传性皮肤病[1]。该病是一种罕见遗传病,发生率约为1/5万活产儿[2]。病人水疱、血疱可发生于全身皮肤及黏膜任何部位,疱大而松弛,稍摩擦即破损呈糜烂面,伴大量渗液渗血;EB有多种常见并发症如营养不良、贫引用信息赵小丹,周旋,曹春艳.1例先天性大疱性表皮松解症伴贫血病人的护理[J]     

64例先天性梅毒新生儿的护理

[目的]总结先天性梅毒新生儿的护理措施。[方法]回顾性分析64例先天性梅毒新生儿的临床资料。[结果]本组病人经1周～2周治疗和护理,康复47例,好转16例,死亡1例;16例好转新生儿经后续治疗1周～2周后全部康复。[结论]加强先天性梅毒新生儿的护理有利于预后。     

21例先天性唇腭裂新生儿的护理体会

[目的]总结先天性唇腭裂新生儿的护理体会.[方法]回顾性分析21例先天性唇腭裂新生儿的临床资料.[结果]本组21例先天性唇腭裂新生儿住院期间均未发生上呼吸道感染、新生儿肺炎、窒息等并发症,母乳喂养率95%.[结论]加强先天性唇腭裂新生儿的护理有利于预防并发症的发生.     

104例先天性心脏病病人行介入封堵治疗的护理

[目的]总结先天性心脏病病人行介入封堵治疗的护理。[方法]对104例先天性心脏病病人行介入封堵治疗,同时加强术前护理、术后心电监护、手术肢体制动与观察、饮食护理、体温监测、并发症的观察与防治等。[结果]104例病人均成功行介入封堵治疗,术后并发心律失常8例,手术穿刺部位渗血1例,假性动脉瘤1例,经治疗和护理后,均恢复正常,顺利出院。[结论]加强先天性心脏病病人行介入封堵治疗的护理,是手术成功的保证。     

Epidermolysis bullosa: a case study in transport, treatment, and care.

There are skin rashes, lesions, and disorders in the neonatal period that require emergent assessment and consultation. A neonate presented with epidermolysis bullosa and provided an opportunity for learning about this condition and various dermatologic resources, primarily DermAtlas. The neonate with suspected epidermolysis bullosa that is delivered in a community setting usually requires transport to a neonatal intensive care unit with pediatric subspecialty care. A case study involving the transport of a neonate with this condition is reviewed, followed by a discussion of the etiology, incidence, pathogenesis, diagnosis, and nursing care before and during transport and parental considerations. The resources available in the neonatal community, primarily DermAtlas, for the identification of epidermolysis bullosa and other dermatological conditions is explored.     

Epidermolysis bullosa. Part 1: causes, presentation and complications

This article is the first in a series of three focusing on the causes, clinical presentation, complications and care of adult patients affected by epidermolysis bullosa (EB), a group of rare genetic skin fragility disorders. Although the condition is rare, in some cases it presents extreme challenges both to those affected and those involved in the care of the EB patient; therefore, these articles may have relevance for other long-term disorders. While there is a wealth of information regarding the 'science' of EB there is dearth of information regarding the care of the adult EB patient, and this series of articles will endeavour to fill that gap. This article focuses mainly on those patients affected with the most severe form of EB found in the adult group, recessive dystrophic epidermolysis bullosa; with the part two looking at the care of the adult with EB from the nursing perspective, including wound management, and the experiences of a specialist EB psychotherapist being presented in the final article of the series. Readers will thus have an opportunity to gain an overall view of this difficult condition.     

重症药疹病人的临床护理

[目的]探讨重症药疹病人的临床护理措施。[方法]总结18例重症药疹病人的临床护理经验,护理措施包括：密切观察病情变化,做好皮肤、黏膜护理,指导合理饮食,预防感染和合并症,心理护理和健康教育等。[结果]18例病人均痊愈出院。[结论]重症药疹的护理重点在于皮肤黏膜护理、预防感染和合并症、营养支持及心理护理。     

238例低体重先天性心脏病婴幼儿行心内直视手术的护理配合

[目的]总结低体重先天性心脏病婴幼儿行心内直视手术的护理配合。[方法]对238例15kg以下低体重先天性心脏病婴幼儿行心内直视手术,同时加强护理配合。[结果]238例患儿手术均获成功,227例完全治愈出院,8例心脏复合畸形患儿术后临床症状缓解、生活质量得到提高,3例死于肺部感染。[结论]加强低体重先天性心脏病婴幼儿行心内直视手术的护理配合是手术成功的保证。     

Cord blood platelet gel for the treatment of inherited epidermolysis bullosa

The management of patients affected by epidemolysis bullosa requires an integrated approach involving different specialties. A cornerstone of clinical management is the prevention and treatment of mechanobullous ulcerations of the patient’s skin, which significantly impact the quality of life and can be the cause of septic and neoplatic complications. This article describes the preliminary clinical evaluation of the use of allogeneic cord blood platelet gel, a novel blood component obtained from umbilical cord blood of healthy, term neonates, for the treatment of skin ulcers in patients with dystrophic epidermolysis bullosa. The promising clinical results obtained in this small patient group support the development of larger controlled clinical trials to compare the efficacy of platelet gel obtained from cord blood versus traditional platelet gel prepared from adult blood donors and versus current standard approaches of wound care in these patients.     

15例声带麻痹患儿先天性心脏病术后护理

目的:探讨声带麻痹患儿先天性心脏病术后的护理措施。方法:做好插管时期的护理、病情观察及呼吸道的护理,减少患儿在插管过程中的躁动行为,防止损伤喉返神经及预防肺动脉高压危象的发生。撤除呼吸机的配合及撤机后的护理,观察患儿的发音情况,有无声嘶、呼吸困难,掌握正确的喂养方法,防止误吸。结果:15例患儿均恢复良好,转至普通病房继续治疗,最后均顺利出院。结论:针对性的临床护理对改善声带麻痹患儿先天性心脏病术后的预后有着重要的作用。     

自护培训对带T管出院患者家庭护理效果影响

目的:探讨自护培训对带T管出院患者家庭T管护理效果的作用。方法:根据时间段将59例带T管出院患者分为常规组28例和培训组31例。住院期间常规组采用常规护理,培训组在此基础上对患者及其家属进行T管自护培训。比较两组患者T管护理知识知晓情况及T管护理效果。结果:培训组T管知识知晓情况和T管家庭护理效果均显著优于常规组(P0.05,P0.01)。结论:T管自护培训能有效地促进患者掌握T管的护理知识和方法,有利于带T管出院患者家庭T管护理。     

18例小儿麻痹症合并骨折病人的护理

[目的]总结小儿麻痹症合并骨折病人的护理。[方法]对18例小儿麻痹症合并骨折病人加强心理护理、疼痛和肿胀的护理、石膏的护理、饮食护理、功能锻炼等。[结果]18例病人均痊愈出院,未发生护理并发症和护理纠纷。[结论]加强小儿麻痹症合并骨折病人的护理有利于预后。     

脊髓栓系综合征手术后脑脊液漏的观察与护理

[目的]总结脊髓栓系综合征（TCS）病人手术后脑脊液漏的观察与护理。[方法]对21例TCS病人行外科手术治疗后进行体位护理、切口护理、心理护理、饮食护理、皮肤护理等护理措施。[结果]无一例病人发生脑脊液漏,均治愈顺利出院。[结论]TCS病人手术后加强脑脊液漏的观察与护理,严格实施护理措施,可预防脑脊液漏的发生,最大限度地恢复脊髓神经功能。