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Liver and lung transplantation in cystic fibrosis: an adult cystic fibrosis centre's experience |
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| Authors: | S. Sivam Y. Al‐Hindawi J. Di Michiel C. Moriarty P. Spratt P. Jansz M. Malouf M. Plit H. Pleass A. Havryk D. Bowen P. Haber A. R. Glanville P. T. P. Bye |
| Affiliation: | 1. Department of Respiratory and Sleep Medicine, Royal Prince Alfred Hospital, Camperdown, New South Wales, Australia;2. Sydney Medical School, University of Sydney, Sydney, New South Wales, Australia;3. Lung Transplantation Unit, St Vincent's Hospital, Sydney, New South Wales, Australia;4. Liver Transplant Unit, Royal Prince Alfred Hospital, Camperdown, New South Wales, Australia;5. AW Morrow Gastroenterology and Liver Centre, Royal Prince Alfred Hospital, Camperdown, New South Wales, Australia;6. Department of Addiction Medicine, Royal Prince Alfred Hospital, Sydney, New South Wales, Australia |
| Abstract: | Liver disease develops in one‐third of patients with cystic fibrosis (CF). It is rare for liver disease to have its onset after 20 years of age. Lung disease, however, is usually more severe in adulthood. A retrospective analysis was performed on nine patients. Three patients required lung transplantation approximately a decade after liver transplant, and another underwent combined liver and lung transplants. Four additional patients with liver transplants are awaiting assessment for lung transplants. One patient is awaiting combined liver and lung transplants. With increased survival in CF, several patients may require more than single organ transplantation. |
| Keywords: | cystic fibrosis lung transplantation liver transplantation lung function test liver function test |