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肝豆状核变性132例颅脑MRI扫描分析
引用本文:喻绪恩,杨任民.肝豆状核变性132例颅脑MRI扫描分析[J].中风与神经疾病杂志,2007,24(1):30-34.
作者姓名:喻绪恩  杨任民
作者单位:安徽中医学院神经病学研究所附属医院,安徽,合肥,230061
摘    要:目的观察肝豆状核变性(hepatolenticular degeneration,HLD)患者颅脑MRI扫描的脑损害特征。方法对我院2003年9月~2005年3月收治的132例HLD患者,人院后在未驱铜治疗前进行颅脑MRI检查,并予统计分析。结果132例HLD的颅脑MRI均有下列一项或一项以上异常改变:壳核异常115例(87.1%),脑干异常53例(40.1%),丘脑异常44例(33.3%)等。结论这些颅脑MRI异常大都与临床表现相符,MRI的异常表现对HLD的早期诊断及预后均具有重要意义。

关 键 词:肝豆状核变性  磁共振成像
文章编号:1003-2754(2007)01-0030-05
修稿时间:2006-08-26

132 cases brain MR imaging of hepatolenticular degeneration
YU Xu-en,YANG Ren-min.132 cases brain MR imaging of hepatolenticular degeneration[J].Journal of Apoplexy and Nervous Diseases,2007,24(1):30-34.
Authors:YU Xu-en  YANG Ren-min
Institution:Institute of Neurolo- gy,Affiliated Hospital ,Anhui College of Traditional Chinese Medcine , Hefei 230061 ,China
Abstract:Objective To report 132 cases brain MR imaging of hepatolenticular degeneration.Methods 132 cases brain MR imaging of hepatolenticular degeneration were collected from Institute of Neurology,Affiliated Hospital,Anhui College of Traditional Chinese Medcine from September,2003 to March,2005.The patients were chosen before they had been treatment.Results Abnormal signals on brain MRI were found in 132 cases:in nu- cleus lenfiformis,115 cases(87.1%),in the brain stem,53(40.1%),in thalamus,44(33.3%),et al.Conclusion The abnormal signals on brain MRI accord with clinical symptoms.Brain MRI are of great significance in diagnosis and prognosis of hepatolenticular degeneration.
Keywords:Hepatolenticular degeneration  MRI
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