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结节性硬化病人功能区致痫皮质结节的手术处理(附9例临床分析)
引用本文:刘仕勇,安宁,杨辉,杨梅华,候智,魏宇佳,张伟,张琴,蔡方成.结节性硬化病人功能区致痫皮质结节的手术处理(附9例临床分析)[J].立体定向和功能性神经外科杂志,2009(4).
作者姓名:刘仕勇  安宁  杨辉  杨梅华  候智  魏宇佳  张伟  张琴  蔡方成
作者单位:第三军医大学新桥医院神经外科、全军癫痫病诊治中心;重庆医科大学附属儿童医院神经内科;
基金项目:重庆市科技计划项目(编号:2008BB5032)
摘    要:目的探讨结节性硬化(tuberous sclerosis,TS)病人功能区致痫皮质结节的手术适应证、手术方式和预后。方法回顾性分析了我院手术治疗9例功能区致痫皮质结节的经验。4例术前已出现功能障碍的功能区皮质结节,术中予以直接切除结节。其余5例病人在唤醒麻醉状态下电刺激病人语言区、运动区和感觉区,其中4例病人显示皮质结节已无功能,予以切除结节;1例病人其结节部分区域存在反应,切除无功能区域后在残余皮质结节边缘行孤立手术。结果本组随访1~5年,平均3年。9例病人中有6例获得I级(Engel分级),2例获得Ⅱ级,1例为III级。平均智商(IQ)从术前的67.4分提高到75.1分。本组3例病人出现暂时性的并发症,未出现新的永久性神经功能损害。结论TS功能区致痫皮质结节可以采取切除性手术为主的处理策略。

关 键 词:难治性癫痫  结节性硬化症  功能区皮质结节  外科治疗  儿童癫痫  

Surgery of cortical tubers of tuberous sclerosis in functional areas
Liu Shiyong,An Ning,Yang Hui,et al..Surgery of cortical tubers of tuberous sclerosis in functional areas[J].Chinese Journal of Stereotactic and Functional Neurosurgery,2009(4).
Authors:Liu Shiyong  An Ning  Yang Hui  
Institution:Liu Shiyong,An Ning,Yang Hui,et al.Department of Neurosurgery,Xinqiao Hospital of Third Military Medical Uuniversity,Chongqing,400037
Abstract:Objective To investigate the surgical procedures and outcomes for epileptogenic cortical tubers of tuberous sclerosis(TS)in functional areas.Methods Surgery of 9 TS patients with epileptogenic cortical tubers in functional areas were reviewed.Epileptogenicc cortical tubers in functional areas were resected directly when the patient had neurodysfunction.Resection procedure was also conducted when cortical tubers in functional areas showed no response monitored by cortical electrical stimulation.Otherwise,the...
Keywords:Intractable epilepsy  Tuberous sclerosis  Functional area tubers  Surgery  Pediatric epilepsy  
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