右肺巨大腺泡细胞癌合并纵隔严重偏移一例

原发性肺腺泡细胞癌极其罕见,世界卫生组织肿瘤分类把腺泡细胞癌定义为一种向(浆液)腺泡细胞分化的恶性上皮源性肿瘤。它被认为是一种低度恶性的肿瘤。自从1972年Fechner首次报道以来,迄今总共不足30例文献报道。因其罕见故容易与其它肺部肿瘤混淆而误诊。我们报道了1例合并纵隔偏移的原发性肺腺泡细胞癌,女,27岁,右肺巨大腺泡细胞癌,行右全肺切除术,术后随访12个月病情稳定。

Giant acinic cell carcinoma complicated with severe mediastinum deviation:A case report

Primary acinic cell carcinoma(ACC)of the lung is extremely rare.The World Health Organization tumor classification defines ACC as"a malignant epithelial neoplasm that demonstrates some cytological differentiation towards(serous)acinar cells".It is considered to be a low-grade malignant tumor.Since the first case described by Fechner in 1972,less than 30 cases have been reported in the literature.The rarity of this tumor may leads it to be confused with other primary lung tumors and incorrectly diagnosed.We reported a female patient with primary ACC of the lung with mediastinum deviation at age of 27 years received a right pneumonectomy.She was followed up for 12 months postoperatively and remains well.