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Granulomatosis with polyangiitis (Wegener’s) complicated by splenic rupture and severe acute respiratory distress syndrome: A case report
Authors:Yannis Ahmad  Gabrielle Morawietz  Hatem Ksouri  Joerg C Schefold  Patrick Zuercher
Institution:1. Intensive Care Unit, HFR Hôpital Cantonal Fribourg, Fribourg Switzerland ; 2. Department of Intensive Care Medicine, Inselspital, Bern University Hospital, University of Bern, Bern Switzerland
Abstract:Even in the absence of disease‐specific radiological signs of granulomatosis with polyangiitis (GPA), severe intrapulmonary GPA may be present. Rapidly establishing the diagnosis with a confirmatory biopsy is key to initiate lifesaving therapy.
Keywords:ARDS  ECMO  granulomatosis with polyangiitis  GPA  Wegener''s
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