肌萎缩侧索硬化症患者的临床与神经电生理特点分析

目的：探讨肌萎缩侧索硬化症（ALs）患者的临床特点以及肌电图（EMG）和神经传导检测对ALS的诊断价值。方法：对56例ALS患者回顾性分析其临床特点、神经传导检测及其胸锁乳突肌、下胸段脊旁肌及肢体肌的EMG资料。结果：56例患者均呈广泛神经原性损害，胸锁乳突肌EMG异常率为89％，胸段脊旁肌EMG异常率为77％。两者异常率均低于上、下肢肌EMG的异常率（分别为100％，91％）。结论：早期EMG及神经传导检测有助于ALS的早期确诊，行胸锁乳突肌及下胸段脊旁肌EMG检测对ALs的诊断及鉴别诊断有重要价值。

Aalysis of electroneurophysiological and clinical characteristics in patients with amyotro- phic lateral sclerosis

Objective： To investigate the features of clinical electromyography（EMG） and nerve conductive velocity（NCV） in patients with amyotrophic laterial sclerosis（ALS）and explore its diagnostic value for ALS. Methods：Fifty-six patients with ALS during 2005 to 2013 were observed retrospectively about their clinical festures,routinue electromyography（EEG） on limbs, sternoeleidomastoid, lower tho- racic paraspinal muscles and nerve conductive velocity. Results：Extensive neurogenie damage was discov- ered in 56 patients with ALS. The abnormality rate of EMG of sternocleidomastoid muscles was 89~, （The abnormality rate： 77~f00 of EMG of thoracic paraspinal muscles was lower than that of upper and lower limb muscles （100%, 91% ）. Conclusion： Early EMG and nerve conductive velocity examination are helpful for early ALS diagnosis. EMG examination for sternocleidomastoid muscles and lower thoracic pa- raspinal muscles plays an important role in ALS diagnosis and differential diagnosis.