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Kartageners综合征伴细支气管炎:影像诊断及随访
引用本文:王立非,关玉宝,顾莹莹,曾庆思,陈苓,张超亮,何建行,钟南山.Kartageners综合征伴细支气管炎:影像诊断及随访[J].中国医学影像技术,2009,25(11):2040-2042.
作者姓名:王立非  关玉宝  顾莹莹  曾庆思  陈苓  张超亮  何建行  钟南山
作者单位:王立非(广州中医药大学祈福医院放射科,广东,广州,511495);关玉宝,曾庆思,陈苓,张超亮(广州医学院第一附属医院放射科,广东,广州,510120);顾莹莹(广州医学院第一附属医院病理科,广东,广州,510120);何建行,钟南山(广州呼吸病研究所,广东,广州,510120) 
摘    要:目的 探讨Kartagener综合征(KS)与细支气管炎的关系.方法 回顾性分析24例KS的临床特点、胸部和鼻旁窦的影像学及病理表现.结果 ①24例KS中,19例均有支气管扩张、全内脏转位、鼻旁窦炎三联征,1例有支气管扩张和鼻旁窦炎,4例有全内脏转位和支气管扩张.临床症状均为反复咳嗽、咳痰、活动后气促,肺部均可闻及湿罗音,22例肺过度通气.②22例胸部DR、18例CT显示两肺弥漫分布2~5 mm的微小结节影,胸部HRCT可见线样征和树芽征,14例(58.33%)表现类似弥漫性泛细支气管炎;20例(83.33%)有鼻旁窦炎.③8例病理确诊为弥漫性泛细支气管炎,病理特点为终末细支气管和呼吸性细支气管管壁增厚,慢性炎细胞浸润;其中2例透射电镜下可见纤毛的内侧臂缺失,其中1例伴有纤毛畸形、融合成团.结论 KS主要表现为支气管扩张、内脏转位、鼻旁窦炎三联征,细支气管炎应作为KS的特征性表现之一,KS也可伴发弥漫性泛细支气管炎.

关 键 词:Kartagener综合征  细支气管炎  诊断显像
收稿时间:2009/4/16 0:00:00
修稿时间:2009/5/11 0:00:00

Bronchiolitis in Kartagener syndrome: imaging diagnosis and following up
WANG Li-fei,GUAN Yu-bao,GU Ying-ying,ZENG Qing-si,CHEN Ling,ZHANG Chao-liang,HE Jian-xing and ZHONG Nan-shan.Bronchiolitis in Kartagener syndrome: imaging diagnosis and following up[J].Chinese Journal of Medical Imaging Technology,2009,25(11):2040-2042.
Authors:WANG Li-fei  GUAN Yu-bao  GU Ying-ying  ZENG Qing-si  CHEN Ling  ZHANG Chao-liang  HE Jian-xing and ZHONG Nan-shan
Institution:Department of Radiology, Clifford Hospital of Guangzhou University of Traditional Chinese Medicine, Guangzhou 511495, China;Department of Radiology, the First Affiliated Hospital, Guangzhou Medical College, Guangzhou 510120, China;Department of Pathology, the First Affiliated Hospital, Guangzhou Medical College, Guangzhou 510120, China;Department of Radiology, the First Affiliated Hospital, Guangzhou Medical College, Guangzhou 510120, China;Department of Radiology, the First Affiliated Hospital, Guangzhou Medical College, Guangzhou 510120, China;Department of Radiology, the First Affiliated Hospital, Guangzhou Medical College, Guangzhou 510120, China;Guangzhou Institute of Respiratory Diseases, Guangzhou 510120, China;Guangzhou Institute of Respiratory Diseases, Guangzhou 510120, China
Abstract:
Keywords:Kartagener syndrome  Bronchiolitis  Diagnostic imaging
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