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Syndromic presentation of a pleuropulmonary blastoma associated with congenital cystic adenomatoid malformation. A case report |
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| Authors: | Nur Samina Badr Riem Sandoval Claudio Brudniki Adele Yeh Albert |
| Affiliation: | a Department of Pathology, New York Medical College, Westchester Medical Center, Valhalla, NY 10595, USA b Department of Pediatric-oncology, New York Medical College, Westchester Medical Center, Valhalla, NY 10595, USA c Department of Radiology, New York Medical College, Westchester Medical Center, Valhalla, NY 10595, USA |
| Abstract: | Pleuropulmonary blastoma (PPB) is a rare malignant mesenchymal pediatric tumor with a well-recognized association with congenital cystic adenomatoid malformation (CCAM). Recently, it has been described in a patient with CCAM, multiple jejunal polyps, and cystic nephroma. We describe a similar case of a unique presentation of PPB, arising in association with CCAM and with a history of intussception caused by multiple small bowel polyps. |
| Keywords: | Pleuropulmonary blastoma Cystic adenomatoid malformation Brain metastasis Hamartomatous polyps Recurrent intussusception |
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