Unilateral occipital hyperhidrosis following Chiari I decompression: case report and a review of the literature

Introduction Paroxysmal unilateral cephalic hyperhidrosis is a rare disorder of the autonomic nervous system.Case report We report an adult male who developed this disorder almost 20 years after posterior fossa decompression for Chiari I malformation with syringomyelia as a child. Further, the patient presented with spastic diplegia. To date, this patient has refused further operative intervention. The medical literature is reviewed regarding this unusual phenomenon.Conclusion To our knowledge, hyperhidrosis of the occiput has not been previously reported in a patient with Chiari I malformation with an associated syringomyelia.