结节性硬化病的CT诊断

目的:探讨结节性硬化(TS)的病因与诊断标准以及CT诊断、分析思路和鉴别诊断。方法:采用CT平扫和增强扫描方法,对3例患者行头部及肾脏检查。结果:3例中伴室管膜下巨细胞星形细胞瘤1例,伴双肾血管平滑肌脂肪瘤1例,另1例孕妇伴双肾血管平滑肌脂肪瘤破裂出血。结论:CT检查对于TS有其特征性表现,基于本病多器官的组织缺陷和错构瘤为特征的系统性疾病特点,优化扫描方案是提高诊断正确率的关键。

CT Diagnosis of Bourneville''s Disease

Objective To study the etiopathogenisis,diagnostic criteria,CT diagnosis,analysis method and differential diagnosis of Bourneville's disease. Methods 3 patients’ brains and kidneys were scanned with CT plain and enhanced scans. Results In 3 cases, there was one case associating with subependymal giant cell astrocytoma and one case associating with angiomyolipoma of both kidneys, another pregnant woman associating with angiomyolipoma break of both kidneys. Conclusion Bourneville’s disease has characteristic appearance in CT scan. Because it is the systemic disease of multi-organic architecture impairmen and hamartoma , the key point of improving correct rate is optimize scanning plan.