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不典型眼肌型重症肌无力的临床特点
引用本文:徐肖,狄晴.不典型眼肌型重症肌无力的临床特点[J].临床神经病学杂志,2011,24(4).
作者姓名:徐肖  狄晴
作者单位:南京医科大学附属脑科医院神经内科,210029
摘    要:目的研究不典型眼肌型重症肌无力(OMG)的临床特点。方法回顾性分析29例不典型OMG患者的临床资料。结果本组患者表现为上眼睑下垂3例,单眼1条眼外肌瘫痪15例,双眼3条眼外肌瘫痪1例,单眼全部眼外肌瘫痪1例,辐辏障碍2例,单眼眼轮匝肌瘫痪1例,类似眼病表现6例(复视4例、眼部不适和视物模糊2例,均无眼外肌瘫痪);有晨轻暮重表现12例(41.4%)。新斯的明试验阳性26例(89.7%),低频重复神经电刺激阳性8例(27.6%),单纤维肌电图(SFEMG)异常23例(79.3%)。患者早期均被误诊。经泼尼松和/或胆碱酯酶抑制剂治疗,症状消失26例(89.7%),显著改善3例(10.3%)。结论不典型OMG患者的临床特点为受累眼肌少,症状局限,表现晨轻暮重的比率低。新斯的明试验和SFEMG检查可确诊。

关 键 词:眼肌型重症肌无力  不典型  临床特点  

Clinical features of atypical ocular myasthenia gravis
XU Xiao,DI Qing.Clinical features of atypical ocular myasthenia gravis[J].Journal of Clinical Neurology,2011,24(4).
Authors:XU Xiao  DI Qing
Institution:XU Xiao,DI Qing.Department of Neurology,Brain Hospital Affiliated to Nanjing Medical University,Nanjing 210029,China
Abstract:Objective To study the clinical features of atypical ocular myasthenia gravis(OMG). Methods The data of 29 patients with atypical OMG were retrospectively analyzed. Results In this group,3 cases had ptosis,15 cases had a ophthalmoplegia,and 1 case had 3 ophthalmoplegia in both sides,1 case had complete ophthalmoplegia in one side,2 cases had convergence disorder,1 case had paralysisofrbicularis in one side,6 cases had similarity eye disease(4 cases had double vision,and 2 cases had only complained of eye di...
Keywords:ocular myasthenia gravis  atypical  clinical features  
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