Askin瘤的影像诊断

目的:分析8例Askin瘤的影像征象。材料和方法:回顾性分析8例Askin瘤的胸部平片、B超和CT资料。年龄13~62岁,平均29.8岁。全组均拍摄正侧位胸片和CT扫描,6例胸壁肿瘤行B超检查。全组均经病理组织学和免疫组织化学检查证实。结果:6例原发于胸壁软组织,肿瘤较小(平均大小3cm),术后半数近期复发,复发灶平均大小为5.5cm。2例原发于纵隔,肿瘤平均大小为7cm。瘤实质主要为软组织,散在液化、坏死或出血。CT增强后扫描呈不规则强化。5例受累胸膜表现为不规则状、结节状增厚。结论:Askin瘤典型影像表现为胸壁、胸膜和纵隔病灶相互融合成巨大肿块。因此,面对青少年患者的胸部软组织肿瘤,鉴别诊断时应考虑到Askin肿瘤。

Imaging Diagnosis of Askin Tumor

Purpose:We present the imaging features in eight patient with Askin tumor.Materials and Methods:There was a retrospective analysis of the imaging results from8patients with askin tumor.The average age was29.8years(ranging from13to62years).At diagnosis,all patients underwent chest CT,chest X-ray(R)and.Six had US.The diagnoses were confirmed histologically and immunohistochemically(n=8).Results:The tumous were originated in soft tissues of chest wall in six debutant patients,The tumors were mainly small(mean size:3cm).After surgery from1to3month,half of tumors were re-curred,which were large(mean size:5.5cm).There were mediastinal involvement in two cases,the tumors were large(mean size:7cm).All tumors were irregular,heterogeneous,had hemorrhage or necrosis and had variable contrast enhancement on CT.Five patients showed pleural nodular irregular involvement with direct infiltration of mediastinum and adjacent rib and muscle.Conclusion:Askin tu-mor typically manifest as large tumors involving mediastinium the chest wall and pleura.The askin tumor should be included in the differential diagnosis on aggressive soft tissue tumors in young patients.