石骨症的X线分析

目的：分析石骨症的影像学表现。方法：9例石骨症患者经胸部、头颅、骨盆、脊柱、股骨、胫腓骨、尺桡骨及双手骨X线摄影检查,对全部患者的X线照片结合文献复习进行分析。结果：石骨症的基本X线表现为全身骨质密度普遍性增高,皮质增厚,髓腔变窄甚至消失,较具特征性的X线征象有：椎体＂夹心蛋糕＂征;髂骨翼＂同心环状＂征;骨中骨征;管状骨干骺端见浓淡交替横纹影;长骨塑形障碍显示棒球杆征,骨膜新生骨形成。结论：该患者是一种罕见的遗传性疾病,可依据其特征性X线表现进行确诊和鉴别诊断。

Roentgenographic Analysis of Osteopetrosis

Objective To analyze the roentgenographic findings of the osteopetrosis. Methods Nine patients with clinically suspected osteopetrosis underwent the X-ray examinations of the chest, skull, pelvis, vertebral column, femur, tibiofibula, bones of upper limb and bilateral handbone. The roentgenographs of all patients were analyzed together with review of the literature. Results The basic image feature of osteopetrosis is bone density increased notably, cortible bone thickening, cavum ossis narrowing or occluded and mark X-ray signs include sandwich change in back bone,concentric rings change in pelvis, bone within a bone change, bright-dark alternation transverse striation in metaphysis of tubiform bone,baseball club appearance due to modelling deformity of long bones and periosteal new bone formation. Conclusion Osteopetrosis is a rare inherited disorder. Its mark roentgonographic findings are important evidence for performing the definite diagnosis and differential diagnosis.[Chinese Medical Equipment Journal, 2009,30（9）： 75-76,78]