阿洪病1例

  报道1例发生于双手、足指（趾）的阿洪病。患者男，32岁，因“双侧手指、足趾末端畸形缩窄伴痒痛10余年”就诊。皮肤科检查：双侧手指、足趾末端可见横行皲裂及明显缩窄环，右手环指收缩带远端软组织已脱落。皮损组织病理示瘢痕组织形成，弹力纤维染色提示弹力纤维断裂减少。DR正位片：右手环指远节指骨缺如，左手小指远节指骨屈曲畸形。诊断：阿洪病。治疗：双手缩窄带处分别用复方倍他米松注射液7 mg、醋酸曲安奈德注射液 40 mg行软组织内封闭各2次；外用多磺酸粘多糖乳膏，2次/d。治疗8个月后皮损较前软化，痒痛感较前减轻。

A case of ainhum disease

 A case of ainhum on both hands and feet was reported. A 32-year old male presented with coarctation of bilateral distal fingers and toes with itching and pain for more than 10 years. Dermatological examination showed chapped and constricted rings were seen on both fingers and toes, and the distal tissue of the right index finger had been fallen off. Pathology showed scar formation with broken elastic fibers. DR showed that the distal phalangeal bone of the right index finger was missing and the left little finger’s distal phalanx was malformed. According to the clinical features and laboratory tests, diagnosis of ainhum was made. The patient was given intralesional betamethasone 7 mg and triamcinolone acetonide acetate 40 mg for 2 times respectively, and polysulfonate mucopolysaccharide cream was used twice daily. After 8 months, the contracted bands were softened and the symptoms were alleviated.