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| 儿童进行性骨化性肌炎5例分析 | |
| 引用本文： | 胡冰,李彩凤,邝伟英,王江,韩彤昕,何晓琥. 儿童进行性骨化性肌炎5例分析[J]. 首都医科大学学报, 2008, 29(6): 766-769 |
| 作者姓名： | 胡冰 李彩凤 邝伟英 王江 韩彤昕 何晓琥 |
| 作者单位： | 首都医科大学附属北京儿童医院内科;首都医科大学附属北京儿童医院内科;首都医科大学附属北京儿童医院内科;首都医科大学附属北京儿童医院内科;首都医科大学附属北京儿童医院内科;首都医科大学附属北京儿童医院内科 |
| 摘 要： | 目的探讨进行性骨化性肌炎的临床特点、影像学表现、临床诊断与治疗方法。方法回顾性分析5例进行性骨化性肌炎患儿的临床表现、影像学改变、诊断及加重病情的诱因。结果5例患儿的发病年龄在出生后7 d～11岁,特点为反复出现身体局部组织肿块、骨化并伴有邻近关节活动障碍,特征性的指、趾短小畸形以及影像学的相应改变。病情呈进行性加重,外伤、局部刺激可加速病情进展。结论进行性骨化性肌炎系少见的常染色体显性遗传病,可通过临床表现及特征性指、趾短小畸形进行早期诊断,易误诊而影响疾病进程。目前无特殊治疗方法,重点在于早期诊断及避免加重疾病的诱因。 |
| 关 键 词： | 骨化性肌炎 指/趾 畸形 |
| 收稿时间： | 2008-08-12 |
Analysis on Five Pediatric Patients with Myositis Ossificans Progressiva |
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| Hu Bing,Li Caifeng,Kuang Weiying,Wang Jiang,Han Tongxin,He Xiaohu. Analysis on Five Pediatric Patients with Myositis Ossificans Progressiva[J]. Journal of Capital Medical University, 2008, 29(6): 766-769 | |
| Authors: | Hu Bing Li Caifeng Kuang Weiying Wang Jiang Han Tongxin He Xiaohu |
| Affiliation: | Department of Internal Medicine;Beijing Children's Hospital;Capital Medical University |
| Abstract: | Objective To investigate the clinical characteristic,image manifestation,diagnosis and the therapeutic methods of the myositis ossificans progressiva(MOP).Methods Five pediatric patients with MOP were reported.The clinical manifestation,changes in imageology,diagnosis,and the motivation of aggravation were analyzed by using retrospective analysis.The literatures relevant to MOP were reviewed.Results The average age of onset ranges from 7 to 11 years old in all 5 cases(4 boys and 1 girl).MOP in all the patie... |
| Keywords: | myositis ossificans digiti malformation |
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