原发性免疫缺陷症(附11例报告)

4例相当于严重联合免疫缺陷症,胸腺皮质全部为脂肪组织,髓质内无胸腺小体,其他各脏器内无淋巴滤泡或淋巴细胞。另4例每例各不相同,多数与遗传因素有关。余3例见皮髓质不能区分,小叶由正常结构的大血管及间隔分割,中心可见透明粉染小团,周围不见同心圆排列的上皮细胞及胸腺小体,相当于Borzy分类中的Partial Dysplasia。

Primary Immunodeficiency A report of 11 cases

Four cases reported in this paper are equivalent to severe combined immumodeficiency, All the thymic cortex turned into fat tissues, There are no hasstall Corpuscles in the medula and no lymph follicle and lymph cells in other internal organs; Other four Cases had different changes but most of them had relation to genetie factors. In the rest three cases cortex and medula could be distinguished, lolubes were seperated by the large blood vessels which had nomal Structure. The Little transparent ball—Like masses dyed with pink could be seen at the middle of lobules. and around them there were no epitheliae cells and hassall corpuscles arranged in concentric circles, eguivalent to the partiae dysplasia according to the alassification of Borzy