| 掌跖角化-牙周破坏综合征临床诊断与治疗 |
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| 引用本文： | 甘红,孙菲,张富强. 掌跖角化-牙周破坏综合征临床诊断与治疗[J]. 临床口腔医学杂志, 2012, 28(1): 42-45 |
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| 作者姓名： | 甘红 孙菲 张富强 |
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| 作者单位： | 上海交通大学医学院附属第九人民医院口腔修复科;上海市口腔医学重点试验室 上海200011 |
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| 基金项目： | 上海市重点特色学科建设项目资助（T0202）;上海市科学技术委员会资助（08Dz2271100） |
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| 摘 要： | 目的：了解掌跖角化一牙周破坏综合征（PLS）临床诊断与治疗。方法：收集并调查一例掌跖角化一牙周破坏综合征病例,进行家谱分析,对其进行全口义齿修复。并对相关文献进行回顾。结果：掌跖角化一牙周破坏综合征是一种罕见的以严重牙周组织破坏及掌跖、膝盖、肘部等部位皮肤过度角化为特征的常染色体隐性遗传病,发病年龄早,最终可导致全口牙列缺失。全口义齿修复可获得较满意的效果。结论：早期发现、早期治疗对改善PLS的预后是非常重要的。
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| 关 键 词： | 掌跖角化一牙周破坏综合征 常染色体隐性遗传 牙列缺失 全口义齿 |
Clinical diagnosis and treatment in Papillon-Lefevre Syndrome. |
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| GAN Hong , SUN Fei , ZHANG Fu-qiang. Clinical diagnosis and treatment in Papillon-Lefevre Syndrome.[J]. Journal of Clinical Stomatology, 2012, 28(1): 42-45 |
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| Authors: | GAN Hong SUN Fei ZHANG Fu-qiang |
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| Affiliation: | GA N Hong, SUN Fei, ZHA NG Fu-qiang. Depart-ment of Prosthodontics , Ninth Peoples Hospital, School of Medicine, Shanghai Jiaotong University, Shanghai Key Laboratory of Stamatology , Shanghai 200011, Chino. |
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| Abstract: | Objective： To understand clinical diagnosis and treatment in Papillon-Lefevre syndrome （PLS）. Method： This paper described a case of PLS, performed genealogies analysis and complete denture restoration, then briefly reviewed the relevant literature. Result： Papillon-Lefevre syndrome is a rare autosomal recessive disorder, characterized by hyperker- atosis involving the palms, soles,elbows,knees and severe early-onset periodontitis,finally leading to loss of teeth. Conclu- sion： Early detection, early treatment is the key to improve the prognosis of PLS. |
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| Keywords: | Papillon.Lefevre syndrome autosome recessive disease edentulous complete denture |
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