胸膜上皮样血管内皮瘤的研究进展 |
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引用本文: | 王发平,范瑛琪,毛辉. 胸膜上皮样血管内皮瘤的研究进展[J]. 国际呼吸杂志, 2016, 0(11): 854-858. DOI: 10.3760/cma.j.issn.1673-436X.2016.11.012 |
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作者姓名: | 王发平 范瑛琪 毛辉 |
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作者单位: | 四川大学华西医院呼吸内科, 成都,610041 |
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摘 要: | 上皮样血管内皮瘤是一种罕见的血管肿瘤,来源于胸膜的胸膜上皮样血管内皮瘤(pleural epithclioid hemangioendothelioma,PEH)更为罕见.PEH的病因及发病机制尚不清楚,主要临床表现为胸痛、咳嗽和呼吸困难,影像学表现主要为胸腔积液及胸膜增厚,组织学特征主要为上皮样瘤细胞及血管内皮标志物CD31、CD34阳性,目前尚未建立有效的治疗方案.本文就该病的病因、临床特征、诊疗特征及预后进行综述,以提高人们对PEH的认识,加强对其发病机制与诊治的研究.
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关 键 词: | 胸膜肿瘤 上皮样血管内皮瘤 研究进展 |
Recent advances in pleural epithelioid hemangioendothelioma |
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Abstract: | Epithelioid hemangioendothelioma is a rare neoplasm of vascular.Pleural epithelioid hemangioendothelioma (PEH) originating in the pleura has been less frequently described.The etiology of the disease has been unknown.Chest pain,cough and dyspnea are the common symptoms.Computed tomography usually reveals pleural effusion and pleural thickening.Histological examination mainly shows epithelioid cells and positive vascular endothelial markers such as CD31,CD34.Effective treatment has not yet been established until now.To improve our understanding of PEH and strengthen the research of its pathogenesis and treatment,this article reviews the etiology,clinical characteristics,diagnosis criteria,treatment and prognosis of PEH. |
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Keywords: | Pleural neoplasms Epithelioid hemangioendothelioma Research progress |
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