DIFFUSE PLANE XANTHOMATOSIS IN A PATIENT WITH BUDD-CHIARI SYNDROME AND MONOCLONAL GAMMOPATHY |
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Authors: | Mukadder Ko?ak Hatice Kele? Fahri Yakaryilmaz ?nder Bozdo?an Sefa Güliter |
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Affiliation: | From the Department of Dermatology, University of Kirikkale, School of Medicine, Ankara, Turkey.;1From the Department of Internal Medicine, University of Kirikkale, School of Medicine, Ankara, Turkey.;2From the Department of Gastroenterology, University of Kirikkale, School of Medicine, Ankara, Turkey.;3From the Department of Pathology, University of Kirikkale, School of Medicine, Ankara, Turkey. |
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Abstract: | Diffuse plane xanthomas are characterized by the presence of yellowish plaques on the eyelids, neck, upper trunk, buttocks, and flexural folds. Histology shows foamy histiocytes in the dermis. Approximately half of the cases are associated with lymphoproliferative disorders. Budd-Chiari syndrome is an uncommon condition induced by thrombotic or nonthrombotic obstruction of hepatic venous outflow. We present a case of diffuse plane xanthoma in a 62-year-old man who developed normolipemic plane xanthomas coinciding with Budd-Chiari syndrome and monoclonal gammopathy. We review the English-language literature regarding the rare association of xanthomas and Budd-Chiari syndrome. |
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Keywords: | Budd-Chiari syndrome diffuse plane xanthoma monoclonal gammopathy |
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