McCune Albright syndrome - diffuse orbital involvement due to fibrous dysplasia: a case report |
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Authors: | Costanzi Márcio Alberto Velasco e Cruz Antonio Augusto |
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Affiliation: | Departamento de Oftalmologia, Otorrinolaringologia e Cirurgia de Cabe?a e Pesco?o, Faculdade de Medicina, Universidade de S?o Paulo, Ribeir?o Preto, SP, Brasil. marciocostanzi@bol.com.br |
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Abstract: | ![]() Fibrous dysplasia is a benign, slowly progressive bone disorder, in which normal bone is replaced by fibrous tissue. It is called McCune Albright syndrome when associated with skin hyperpigmentation and endocrinological disorders. We report a rare case of McCune Albright syndrome in a boy, who presented bilateral and diffuse involvement of orbits but few external craniofacial distortions. |
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