Occurrence of secondary cystathioninuria in children with inherited metabolic disorders,liver diseases,neoplasms, cystic fibrosis and celiac disease

Secondary cystathioninuria was found in two of 46 children suffering from tumors, leukemia, liver diseases, inherited metabolic disorders, cystic fibrosis and celiac disease. Of these two patients, one had congenital biliary atresia and the other cytomegalovirus infection. Seven further children had only moderately elevated excretion of cystathionine. It is suggested that secondary cystathioninuria is uncommon in the diseases investigated.Dedicated to Professor Dr. A. Wiskott on the occasion of his 80th birthday