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An unusual variant of familial preexcitation
Authors:H J Vidaillet  C S Burton  N M Ramirez  M R Gilbert  V S Behar  D B Hackel  L D German
Affiliation:1. Westmead Clinical School, Faculty of Medicine and Health, The University of Sydney, Sydney, NSW, Australia;2. Department of Cardiology, Westmead Hospital, Sydney, NSW, Australia;3. Department of Cardiology, Sunshine Coast University Hospital, Brisbane, Qld, Australia;4. University of the Sunshine Coast, Brisbane, Qld, Australia;5. School of Medicine, Griffith University, Sunshine Coast University Hospital, Brisbane, Qld, Australia;6. South Western Sydney Clinical School, University of New South Wales, Sydney, NSW, Australia;1. Medical Center, Port-Said University, Port-Said, Egypt;2. Department of Pharmacology and Toxicology, Faculty of Pharmacy, Suez Canal University, Ismailia 41522, Egypt;1. Department of Neurology, Medical University of Vienna, Vienna, Austria;2. Department of Neurology, Christian Doppler Medical Center, Paracelsus Medical University, Salzburg, Austria;1. Pittsburgh Heart, Lung, Blood Vascular Medicine Institute, University of Pittsburgh School of Medicine, PA, USA;2. Bioland Laboratory (Guangzhou Regenerative Medicine and Health Guangdong Laboratory), Guangzhou, Guangdong 510320, China;3. Department of Bioengineering, University of Pittsburgh Swanson School of Engineering, PA, USA;4. Division of Cardiology, Department of Medicine, University of Pittsburgh School of Medicine, PA, USA;1. Division of Cardiac Surgery, University of Pittsburgh Medical Center, Pittsburgh, Pennsylvania;2. Heart and Vascular Institute, University of Pittsburgh Medical Center, Pittsburgh, Pennsylvania;3. Division of Cardiology, University of Pittsburgh Medical Center, Pittsburgh, Pennsylvania
Abstract:
Variants of the preexcitation syndromes including accessory atrioventricular pathways (Wolff-Parkinson-White syndrome), nodoventricular and fasciculoventricular fibers (Mahaim) and atrio-Hisian fibers (Brechenmacher) are well established in the literature. 1 Familial occurrence of Wolff-Parkinson-White (WPW) syndrome has been reported and autosomal dominant inheritance has been proposed.2 We report a family whose unusual features included a unique combination of accessory pathways causing preexcitation and associated findings of excessive lentiginosis and sudden cardiac death.
Keywords:
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