Replacement of the Descending Thoracic Aorta for Massive Aneurysm in Neonatal Marfan Syndrome |
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| Authors: | Giovanni Battista Luciani MD Giuseppe Faggian MD Alessandro Mazzucco MD |
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| Institution: | Department of Cardiovascular Surgeaty, University of Verona Medical School, Verona, Italy |
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| Abstract: | We describe a patient with neonatal Marfan syndrome presenting with massive ascending and descending thoracic aortic aneurysm. Because of rapidly progressive respiratory distress due to tracheobronchial compression, emergency replacement of the descending thoracic aorta with a 12-mm PTFE vascular prosthesis was undertaken at 1 month of age. The postoperative course was complicated by bilateral tension pneumothorax contributing to irreversible respiratory failure. The unique clinico-pathological features and the relevant surgical implications of the case are discussed. (J Card Surg 1994;9:109–114) |
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