肌萎缩型脊髓空洞症的诊治

目的：报告临床表现为肌萎缩型的脊髓空洞症并探讨其发生机理、误诊原因和诊治原则。方法：详细分析６例病例的临床资料。结果：该型病变易被误诊的原因是患者病变早期无感觉功能或植物神经功能异常。结论：本型的空洞可能始发于脊髓前角细胞；ＭＲＩ检查可确定诊断；后颅窝减压和脊髓空洞－蛛网膜下腔分流术是有效的治疗手段；应争取尽早诊治以避免患者产生不可逆的功能损害。

Diagnosis and treatment for syringomyelia manifested muscular atrophy

Objective: To report syringomyelia manifesting muscular atrophy and to discuss its proceeding mechanism, the causes of misdiagnosis and the role of the diagnosis and treatment. Methods: The clinical data of 6 cases were analysed in detail. Results: The causes of misdiagnosis were no sensory disturbance or vegetative nerve functional disturbance in early period of the disease. Conclusions: The cavity may premarily occur at anterior horn of spinal cord in the type of syringomyelia. MRI examination can correct the diagnosis. The effective method of treatment are posterior fossa decompression and syringosubarachnoid shunts, and it should be diagosed and treated as early as possible, to avoid irreversible damage of the spinal cord.