完全型心内膜垫缺损的MRI诊断

目的 评价ＭＲＩ对完全型心内膜垫缺损的诊断价值和限度。方法 对８例（男５例，女３例）患者行自旋回波（ＳＥ）和电影ＭＲＩ诊断。诊断由Ｘ线平片，超声心动图，Ｘ线右心导管加心血管造影以及ＭＲＩ等多种影像学技术作出，其中４例行手术治疗。结果 ＭＲＩ显示心脏各个房室腔扩大，多数以右心房室扩大为著，伴有右心室壁增厚心内膜垫结构消失，４个心腔呈“十”字形直接相通，形成膜部空间隔缺损和Ｉ孔型空间隔缺损，二，三尖瓣

Magnetic resonance imaging in complete type endocardial cushion defect

Objective To evaluate the value and limitation of magnetic resonance imaging (MRI) in complete type endocardial cushion defect (CTECD). Methods Eight patients (male 5,female 3) were scanned by MRI with ECG gated spin echo (SE) and gradient echo (GE) cine techniques. The diagnosis of CTECD was made by X ray plain film, echocardiography, X ray right cardiac catheterization and angiocardiography ,as well as MRI. four patients were treated with operation. Results Every chamber of the heart was enlargerd, more serious in the right atrium and ventricle, with thickening of right ventricular wall on MRI in majority of cases. The endocardial cushion disappeared, so the four chambers of the heart were directly connected with each other, and presented a cross shape. Ventricular septal membrane defect and type I atrial septal defect were depicted also. The normal structure of mitral and tricuspid valves were not intact. There were 6 cases with pulmonary hypertension,2cases with Tetralogy of Fallot,4 cases with right aorta arch and descending aorta, 1 patient with dextroverted heart and another with persistent left superior vena cava connected with coronary sinus. The cine MRI could directly depict the situation of left right or right left shunt at atrial and ventricular levels, and regurgitation from ventricles to atria, meanwhile the valves were depicted clearly. Conclusions MRI can clearly demonstrate all anatomic deformation and complicated hemodynamic change of CTECD, as well as other coexistent deformations.