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血管内T细胞淋巴瘤一例报道并文献复习
引用本文:罗金梅,张薇,霍真,崔全才.血管内T细胞淋巴瘤一例报道并文献复习[J].白血病.淋巴瘤,2008,17(6):436-438.
作者姓名:罗金梅  张薇  霍真  崔全才
作者单位:中国医学科学院北京协和医院内科,北京,100730;中国医学科学院北京协和医院血液内科,北京,100730;中国医学科学院北京协和医院病理科,北京,100730
摘    要:目的提高对血管内淋巴瘤(IVL)的认识。方法报道一例IVL的临床表现和诊治经过,并进行文献复习。结果以发热、皮疹和嗜血细胞综合征为表现的IVL少见,该例患者经过积极化疗效果不显著,最后死于肝衰竭和消化道出血。结论IVL少见,患者生前诊断困难,病情进展快,预后差。

关 键 词:血管内淋巴瘤  淋巴组织细胞增多症  嗜血细胞性  淋巴瘤  T细胞
收稿时间:2008-03-25;

Intravascular T-cell lymphoma:one case report and Hterature review
LUO Jin-mei,ZHANG Wei,HUO Zhen,CUI Quan-cai.Intravascular T-cell lymphoma:one case report and Hterature review[J].Journal of Leukemia & Lymphoma,2008,17(6):436-438.
Authors:LUO Jin-mei  ZHANG Wei  HUO Zhen  CUI Quan-cai
Institution:LUO Jin-mei, ZHANG Wei, HUO Zhen, CUI Quan-cai. (Department of Internal Medicine, Peking Union Hospital, Peking Union Medical College, Chinese Academy of Medical Sciences, Beijing 100730, China )
Abstract:Objective To improve the recognition of intravaseular lymphoma.Methods One case of intravaseular T-cell lymphoma was reported and the related literatures were reviewed.Results Intravaseulal T-cell lymphoma presenting with fever,rash and haemophagocytie syndrome is rare.Although the patient was given chemical therapy,he was died of liver failure and gastrointestinal bleeding.Conclusion Intravascular T-cell lymphoma is rare,often diagnosed after autopsy and shows a rapidly aggressive course.
Keywords:Intravasculal lymphoma  Lymphohistioeytosis  hemophagocytic  Lymphoma  T cell
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