Coincidence of Total Anomalous Pulmonary Venous Drainage to the Superior Vena Cava,Common Atrium,and Single Ventricle: A Very Rare Condition

Single ventricle defects, including inflow emptying into 1 ventricle, occur at an incidence of 0.05–0.1 per 10,000 live births. The association of total anomalous pulmonary venous drainage (TAPVD) with single ventricle defects is a risk factor for poor outcome. Conversely, common atrium, a rare congenital anomaly, is an endocardial cushion defect. We present a rare case of an unoperated patient with coincidence of a single ventricle defect, TAPVD with direct drainage from the pulmonary veins into the superior vena cava, and common atrium. To the best of our knowledge, such a case has not been previously reported in the literature.