不典型肾血管平滑肌脂肪瘤诊断与治疗

目的 探讨不典型肾血管平滑肌脂肪瘤的误诊原因,提高其诊治水平.方法 回顾性分析20例不典型肾血管平滑肌脂肪瘤患者的临床资料.20例均行B超检查,17例行CT扫描,10例行MRI扫描,8例行IVU检查.5例接受保守治疗,15例接受手术治疗,其中3例行肿瘤剜除术,5例行肾部分切除术,7例行肾癌根治术.结果 B超诊断肾血管平滑肌脂肪瘤12例(12/20),CT诊断肾血管平滑肌脂肪瘤9例(9/17).5例保守治疗者获得随访,肿瘤大小无明显变化,无转移.15例手术治疗者术后病理检查均为肾血管平滑肌脂肪瘤,随访未见肿瘤转移或复发.结论 大部分肾血管平滑肌脂肪瘤可通过B超、CT等影像学检查明确诊断;对于不典型肾血管平滑肌脂肪瘤,术前应仔细分析影像学检查,必要时应根据术中冰冻切片决定手术方案,减少不必要的肾切除.Abstract：Objective To investigate the misdiagnosis causes of atypical renal argiomyolipoma(RAML), and to improve its diagnosis and treatment. Methods We retrospectively analyzed the clinical datas of 20 patients with atypical RAML.Twenty cases made B-ultrasonography,17 cases made CT scan,10 cases made MRI scan,8 cases made IVU examination. of all patients, 5 cases were treated conservatively,15 cases underwent operations, 3 cases underwent tumor enucleation, 5 cases underwent partial nephrectomy, and 7 cases underwent radical nephrectomy. Results The positive diagnosis rate of ultrasonography and CT scan was 60%(12/20) and 53%(9/17). The 5 cases treated conservatively had no change by follow-up, no significant change in tumor size, without metastasis.Fifteen cases underwent operations were confirmed RAML after postoperative pathological examination, no tumor metastasis or recurrence in follow-up. Conclusions The majority of RAML can be diagnosed definitely by ultrasonography and CT scan. As to atypical RAML, we should carefully analyze image information before operation. Necessarily, we can decide operational plan according to frozen section, so as to avoid unnecessary nephrectomy.

Diagnosis and treatment of atypical renal angiomyolipoma

Renal angiomyolipoma Diagnosis Treatment