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1.
目的分析心肌致密化不全患者心电图及临床特点。方法4例患者经超声心动图诊断为心肌致密化不全,描记心电图并进行分析。结果4例患者均有程度不等的心功能不全,心电图记录到频发PVC、VT、VF,AF等心律失常及ST-T改变。结论心肌致密化不全是一种少见的先天性心肌病,以心脏扩大、心力衰竭及室性心律失常等为主要临床特点,心电图及超声心动图具有一定的诊断价值。  相似文献   

2.
特殊类型心肌病——心肌致密化不全的研究进展   总被引:6,自引:0,他引:6  
心肌致密化不全是一种特殊类型的心肌病。现对心肌致密化不全的病因、发病机理、临床及超声心动图特点进行文献综述,旨在为临床诊断及治疗提供客观依据。  相似文献   

3.
心肌致密化不全患者的临床特点及预后   总被引:5,自引:0,他引:5  
目的:通过分析心肌致密化不全患者的临床特点、诊断方法、治疗及预后,以提高临床诊治水平。方法:分析及随访2000年1月~2006年4月住院治疗的17例心肌致密化不全患者的临床资料、治疗及预后。结果:心肌致密化不全特征为海绵状心肌,多发生于左心室。临床表现主要为心力衰竭(纽约心功能分级Ⅱ~Ⅳ级者占88.2%)、心律失常及血栓形成(分别为88.2%与11.8%)。17例中14例为孤立性心肌致密化不全,3例合并其他心血管疾患。17例患者均行超声心动图及心脏磁共振检查,其中13例患者的超声心动图及心脏磁共振检查均明确诊断,另4例经心脏磁共振检查确诊。随访10例患者,3例行心脏移植手术,1例死亡。结论:心肌致密化不全临床表现各异,预后差。超声心动图检查是诊断主要方法,心脏磁共振检查有助于提高诊断水平。  相似文献   

4.
心肌致密化不全临床上罕见,误诊及延迟诊断较多,该文就超声心动图及心脏磁共振检查特征、诊断标准、新进展进行总结,旨在提高对心肌致密化不全的认识和诊断水平.  相似文献   

5.
目的分析心室肌致密化不全患者临床特点、心电图表现、超声心动图特征,为临床进一步认识和诊治心室肌致密化不全提供依据。方法分析2009年~2011年在解放军总医院接受治疗的13例心室肌致密化不全患者,并结合文献复习,讨论该病的临床特点、心电图、辅助检查、治疗及预后。结果心室肌致密化不全可发生于任何年龄,多见于中青年。13例患者中均有不同程度的心功能不全或心律失常,心电图记录到各种心律失常及ST—T改变。超声心动图是诊断心肌致密化不全的主要手段,特异性高,但核磁共振等检查对于部分病例同样重要。结论心室肌致密化不全是一种少见的先天性心肌病,以心脏扩大、心力衰竭及室性心律失常等为主要临床特点,心电图及超声心动图具有一定的诊断价值。  相似文献   

6.
目的分析心肌致密化不全的临床特征。方法对确诊为心肌致密化不全的18例患者的临床表现、心电图、心脏彩超、血清肌钙蛋白、血浆脑钠肽前体(NT-pro BNP)等进行总结、分析。结果心肌致密化不全患者多以胸闷、气短等心衰症状就诊,NYHA分级多Ⅳ级,NT-pro BNP、肌钙蛋白I均有不同程度的增高,心电图示合并有多种心律失常改变;均行心脏彩超检查发现心肌致密化不全的特异性改变,其中累及心尖部7例(39%),累及左室侧、后壁10例(65%)。结论心肌致密化不全患者年龄分布较广,临床表现以心衰表现多见,可合并多种心律失常。心脏彩超多以左心改变多见,为确诊的主要方法。  相似文献   

7.
随着近年来对心肌致密化不全认识的提高,临床报道逐年增多,但仍有许多问题存在争议。现就其病因、发病机制、临床表现、诊断及治疗方面的问题进行探讨。  相似文献   

8.
目的 探讨彩色多普勒超声心动图诊断心肌致密化不全的临床价值.方法 心肌致密化不全11例,年龄11个月~75岁,用GE VIVID7,SEQUOIA 256彩色超声仪,探头频率2.5~4.5MHz,分析其超声特点及临床表现.结果 11例患者左心室不同程度扩大,心肌收缩功能减退,心尖部心肌由两层构成,外层致密心肌边薄,内层心肌呈小梁网状海绵样结构,有丰富的隐窝,海绵样心肌厚度与致密心肌厚度比值为2.5~5.4,彩色多普勒显示隐窝内低速血流与左心室腔相通.结论 左心室心肌致密化不全有明显的超声特征,彩色多普勒超声心动图是惟一的诊断手段.  相似文献   

9.
心肌致密化不全是由于胚胎期心内膜肌小梁致密化过程异常终止导致心室发育不良的先天性心肌病,以心力衰竭、心律失常、血栓形成为主要临床表现,目前临床诊断主要依靠超声心动图、核磁共振,患者的疾病进展和预后差异很大.本文对心肌致密化不全目前的研究进展作一综述,为临床诊断及治疗提供依据.  相似文献   

10.
目的:研究心肌致密化不全患者的临床特征及预后.方法:对超声心动图诊断的心肌致密化不全36例患者,进行症状、心电图、超声心动图及随访等资料分析.结果:36例患者中9例呈家族集聚发病例,19例为散发病例,8例未进行家系筛查.17例以心力衰竭为主要表现,13例以心悸为主要表现,6例无明显症状.随访资料完整者32例,左室进行性增大17例,血栓形成及血栓事件4例,死亡1例.结论:心肌致密化不全主要表现为心力衰竭、心房颤动、缓慢性心律失常,预后较差,有较高的血栓事件.  相似文献   

11.
目的:总结成人心肌致密化不全(NVM)患者的临床特点.方法:回顾性分析25例NVM患者的临床表现、心电图、超声心动图以及心脏磁共振成像资料.结果:25例患者年龄15~75岁,其中男性18(72%)例,女性7(28%)例,其中4例有家族史.首发症状以胸闷气短最为常见共计21例,占84%,19例出现心力衰竭症状,仅1例出现脑栓塞.所有患者均伴有心律失常,类型多样.14例行心脏磁共振成像检查的患者均提示心肌致密化不全,其中6例超声心动图没有提示心肌致密化不全,其部位均累及左心.结论:NVM发病年龄及症状差异很大,主要表现为心力衰竭和心律失常,栓塞事件少见.超声心动图是诊断NVM的基本手段.心脏磁共振成像是诊断的重要辅助手段.  相似文献   

12.
A four month old infant with isolated left ventricular non-compaction was treated with carvedilol. Haemodynamic studies and various types of imaging—including echocardiography, radiographic angiography, magnetic resonance imaging, and single photon emission computed tomography with 201Tl, 123I-β-methyliodophenylpentadecanoic acid (BMIPP), and 123I-metaiodobenzylguanidine (MIBG)—were performed before and 14 months after treatment. Left ventricular ejection fraction increased from 30% to 57%, and left ventricular end diastolic volume, end systolic volume, and end diastolic pressure showed striking reductions during treatment. Left ventricular mass decreased to about two thirds of the baseline value after treatment. Per cent wall thickening increased after carvedilol in the segments corresponding to non-compacted myocardium. A mismatch between 201Tl and BMIPP uptake in the area of non-compaction observed before carvedilol disappeared after treatment. Impaired sympathetic neuronal function shown by MIBG recovered after treatment. Thus carvedilol had beneficial effects on left ventricular function, hypertrophy, and both metabolic and adrenergic abnormalities in isolated left ventricular non-compaction.


Keywords: isolated left ventricular non-compaction; carvedilol; cardiac sympathetic nerve; ventricular remodelling  相似文献   

13.
A 57-year-old woman with syncope was admitted. She had a family history of sudden death: two brothers had died suddenly at the age of 47. Transesophageal echocardiography showed numerous prominent trabeculations and deep intertrabecular recesses in the anterior and lateroapical zones. Isotopic left ventricular ejection fraction was 46%. Cardiac catheterization showed coronary arteries with no angiographic lesions. A prominent trabecular zone and deep intertrabecular recesses were seen in the anterior wall on left ventriculography. Right ventriculography was normal. The diagnosis of isolated noncompaction left ventricular myocardium was established. Continuous 24-h electrocardiographic registry showed episodes of polymorphic ventricular tachycardia. Programmed ventricular stimulation performed at the right ventricular apex with up to three extrastimuli failed to induce ventricular arrhythmias. Treatment with beta blockers was initiated, but short runs of polymorphic ventricular tachycardia persisted. A dual-chamber automatic implantable defibrillator was implanted. We discuss the physiopathology of the arrhythmia. It appears that several factors could be responsible for the malignant arrhythmias in this entity.  相似文献   

14.
Non-compaction of the ventricular myocardium is a cardiomyopathy caused by the arrest of normal embryogenesis of the ventricles. It is classified in isolated non-compaction of the ventricles (most frequently of the left one) and in ventricular non-compaction associated with other congenital anomalies of the endocardium and myocardium, such as obstruction of the right or left ventricular outflow tracts, complex cyanotic congenital heart disease, and coronary artery anomalies. There are controversies regarding the right ventricle non-compaction due to the normally trabeculated shape of its walls.We present a case of severe heart failure with a complex anomaly: biventricular non-compaction, ventricular septal defect and aortic thoracic stenosis.  相似文献   

15.
Isolated noncompaction of ventricular myocardium (INVM) is a genetic cardiomyopathy due to abnormal arrest in endomyocardial embryogenesis between fetal 5th and 8th week. Noncompaction of right ventricle alone is rare. Here we present one such case where a young man presented with progressive right heart failure and atrial fibrillation. Subsequent evaluation by echo and cardiac magnetic resonance imaging confirmed our diagnosis. The cardinal manifestations of INVM are heart failure, arrhythmia, and embolic events and our case presented with former two manifestations. Echocardiographic criteria for diagnosing INVM are discussed.  相似文献   

16.
Isolated noncompaction of the ventricular myocardium (INVM) is an unclassified cardiomyopathy and is thought to be due to arrest of myocardial morphogenesis. Although right ventricular involvement is not uncommon, the correct diagnosis is often difficult by echocardiography. In this report, we describe a patient with INVM in whom magnetic resonance imaging was useful to detect right ventricular morphological and functional abnormalities.  相似文献   

17.
目的探讨成人左室心肌致密化不全的超声心动图特点。方法对45例成人左室心肌致密化不全患者进行超声心动图检查,多切面重点观察左室心肌与心内膜。结果超声心动图检查表明,左室腔内可见异常粗大呈蜂窝状的肌小梁和交错深陷的隐窝,其中34例有心力衰竭症状,3例进行心脏移植,11例患者受累心肌局限在左室心尖部,无任何症状。彩色多普勒可探及隐窝内有血流与心腔相通。结论超声心动图可快速、无创地诊断心肌致密化不全。  相似文献   

18.
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