Clinical analysis of alveolar soft-tissue sarcoma of the uterine cervix: a case report

Alveolar soft part sarcoma （ASPS） is a rare tumor that was originally named by Christopherson in 1952.Until now, fewer than 200 cases have been described in the literature. The ASPS on the uterine cervix is a very rare malignant tumor of the female reproductive organs. Including the first case described by Flint et al2 in 1985, there have been only a few cases reported to date, of which two were in China, and there is a lack of insightful analysis of treatment options. Therefore, to raise awareness of this disease, we performed a detailed literature review, which includes a case encountered by ourselves.     

SEMYXOID ADRENOCORTICAL CARCINOMA PRESENTING AS CUSHING SYNDROME: ONE CASE REPORT

Myxoid change in adrenocortical carcinoma is a rare phenomenon,and no case has been reported in Chinese population to date.We report here a case of myxoid adrenocortical carcinoma presenting as Cushing syndrome with an immunohistochemical study of the tumor and discuss the diagnosis with reference to the current literature.     

Primary cardiac hemangioendothelioma: a case report

Primary cardiac hemangioendothelioma is extremely rare.1-3 Up to now less than twenty cases have been reported in English literature, the data about this kind of cardiac tumors are scanty. In this report, a case of a huge hemangio-endothelioma that arose from the right atrium and was successfully resected is presented.     

CLINWAL NOTES AND CASE REPORTS ADAMANTINOMA OF THE LTPPER JAW REPORT OF A CASE

Adamantinomas usually occur in the jaws and are more frequently found in the lower than in the upper jaw. It is not a common tumour though cases of clinical importance have been reported every now and then chiefiy in the American literature. In China as far as we know this tumour has nof been described although there is evidence that cases* have been noticed judging from the returns of the recent Chinese Medical Association hospital sta- tistical survey(I). The authors have recently had a case of Adaman- tinoma under investigation in a Chinese patient age 22. The past history of the patient is as follows: Teu years ago she fiM poticed that the right side of her face became more prominent and since then the swelling has steadily increased in size. Except for the deformity it gave her no particular trouhle and it was only during the last few years that she rioticed blocking in the right side of her nose and diplopia when looking toward the left side. There was aIso epiplora. The deformity caused a great deal of disIigurement to the patient, so there was no di伍culty in getting her consent to an operahon.     

Primary cardiac hemangioendothelioma: a case report

Primary cardiac hemangioendothelioma is extremely rare.1-3 Up to now less than twenty cases have been reported in English literature, the data about this kind of cardiac tumors are scanty. In this report, a case of a huge hemangio- endothelioma that arose from the right atrium and was successfully resected is presented. CASE REPORT A 36-year-old woman who complained of progressive shortness of breath for two years and being difficult on supine position for 2 months was admitted to the ho…     

Adult primary undifferentiated embryonal sarcoma of the liver: a case report

Undifferentiated embryonal sarcoma of the liver （UESL） was first described by Stocker and Ishak in 1978. It is a rare tumor that most often presents in childhood between 6 to 10 years of age.2 The adult patients diagnosed with UESL often show nonspecific symptoms with normal laboratory results. Ultrasonography, CT, or MRI often reveals a cystic mass. Complete surgical resection plus pre- and/or post-operative systemic chemotherapy offers the possibility of a cure. We report a case of primary UESL in an adult with no specific symptoms, tumor markers, or image results. The diagnosis of the case was based on the resulting pathology from surgery.     

Lymphoepithelial cyst of the pancreas： a case report

BACKGROUND: Lymphoepithelial cyst of the pancreas is a rare lesion of undetermined pathogenesis that had been documented almost exclusively in males. The literature on this entity is limited to reports of single or a small number of cases, METHODS: The case we described herein was compared with a total of 36 cases reported elsewhere. RESULTS: The 37 cases of lymphoepithelial cyst of the pancreas including our case were reviewed, Lymphoepithelial cysts have uniform and distinctive clinicopathologic features.     

Congenital left ventricular diverticulum diagnosed by echocardiography

To the editor:Left ventricular diverticulum is a rare congenital anomaly,and poorly understood.The first patient was described by O'Bryan in 1838) Here we report a case of a 19-year-old young man with isolated huge left ventricular divertivulum He was admitted to our hospital for heart assessment.He had no connective tissue disorders or other systemic anomalies,and there was no signification family history of disease.Transthoracic echocardiography and magnetic resonance imaging (MRI) showed a large outpouching lesion that contained full-thickness myocardium at the anterolateral wall of the left ventricle without any other cardiac defects (Figure 1).Computed tomography angiography showed no significant coronary artery stenosis.This established the diagnosis of isolated left ventricular diverticulum.The man's cardiac function was within normal limits,and a surgical procedure was not indicated.     

Epithelioid angiosarcoma of esophagus

Epithelioid angiosarcomas (EAS) are very uncommon tumors accounting for less than 1％ of all sarcoma and most frequently occur in the skin and subcuits.Primary angiosarcomas in alimentary tract are very rare,especially in esophagus and only one case has been reported in the Chinese literature.1 Evidence-based advice regarding optimal management is lacking.Here,we reported a case of 54-year-old man who was found to have EAS in the esophagus.     

Synchronous granulocytic sarcoma of the breast and spine: a case report and review of the literature

Granulocytic sarcoma or chloroma is a rare tumour derived from myeloid cell precursors. It is generally seen before or after or together with the onset of myelocytic leukaemia. Immunohistochemical staining of myeloperoxidase is necessary for a definite diagnosis of granulocytic sarcoma. Recognition of this entity ensures an early aggressive chemotherapy that causes regression of the tumour.1-3 We present an unusual case of a 40-year-old woman who presented with back pain, numbness in the legs, and fatigue for 2 weeks. She was diagnosed as having synchronous granulocytic sarcomas of the breast and spine, confirmed surgically and histopathologically. After a subsequent systemic chemotherapy the patient was completely asymptomatic during a 20-month follow-up. We also reviewed the literature about the clinical manifestations, diagnosis, treatment, and prognosis of this condition.     

A novel case of Hyper IgE syndrome combined with natural killer cell deficiency

The Hyper IgE syndrome （HIES） is a rare,complex primary immunodeficiency.Here we report a case of HIES combined with natural killer cell deficiency,which has not been previously documented in the literature.Written informed consent was obtained from the patient for publication of this case report and any accompanying images.     

Massive hemoptysis and hemothorax: a rare but fatal complication of intralobar sequestration

Intralobar sequestration (ILS) is an uncommon abnormality that accounts for 75% of all pulmonary sequestrations. Over the years there have been several reports of various presenting signs of which hemoptysis was commonly described, however, massive hemoptysis and hemothorax is extremely rare in literature. We present a case of a 45-year-old man who died of fatal complication from an ILS. This case report shows an uncommon presentation of ILS with massive hemoptysis and hemothorax resulting in a dramatic course of disease and a fatal outcome, and for this reason in the absence of trauma or other causes for massive hemoptysis, hemothorax, or lung hematoma, this possibility should be kept in mind so as to avoid misdiagnosis, and resection of the sequestered tissue should be considered in all patients.

     

Hemorrhagic shock caused by rupture of cystic artery pseudoaneurysm secondary to calculous cholecystitis

Cholecystitis is a common disease in East Asia. Some of the patients developed cystic artery pseudoaneurysm,a rare complication of cholecystitis. Over the past decades, there have been Tess than 20 reports of patients with cystic artery pseudoaneurysm in the literature. Among them, three of the patients had gallbladder perforation which led to hemorrhagic shock,la We report a case of an 88-year-old woman with a cystic artery pseudoaneurysm following an episode of acute cholecystitis.     

Heterotopic gastric mucosa with mild dysplasia in the gallbladder

Heterotopia,also termed as ectopia or choristoma,means the occurrence of normal tissue in an abnormal location.Heterotopic gastric mucosa in gallbladder is very rare and was first reported by Egyedi in 1934;1 it is difficult to make a correct preoperative diagnosis.Our aim is to present this unusual case of heterotopic gastric mucosa together with intestinal metaplasia and mild dysplasia in the gallbladder and to review the literature.     

Ewing''s sarcoma of the maxilla

Primary Ewing's sarcoma of the maxilla is exceedingly rare. Only more than 30 cases have been reported in the English literature.1 As far as we know Ewing's sarcoma of the maxilla has not been reported in the Chinese literature. A case of Ewing's sarcoma of the maxilla is presented and the entity is discussed.     

Multimodality therapy including surgical resection for limited small cell lung cancer.

From 1975 through 1990, 199 patients with limited small cell lung cancer (LSCLC) were subjected to multimodality treatment including surgical resection combined with chemotherapy or chemoradiotherapy in our department. The median postoperative survival time of the 199 patients was 39 months, and the 5-year survival rate was 26%, which was decreased with increase of tumor-stage. In comparison of the survival time of patients in Stage Ⅰ and those in Stage Ⅲa, there was a significant difference (P<0.01). There were no significant differences in survival rate of 3 and 5 years between the patients receiving chemotherapy prior to or after surgical resection. The improvement in survival was documented by surgical resection combined with chemotherapy or chemoradiotherapy for LSCLC. The effect of multimodality treatment is correlated with tumor P-TNM staging, the involvement of lymph node, especially that of the mediastinal lymph node, is a negative factor influencing the prognosis. Surgical resection as an ini     

THE SEASONAL INCIDENCE OF KALA-AZAR IN INFANTS AND ITS SIGNIFICANCE IN RELATION TO THE TRANSMISSION PROBLEM OF THE DISEASE*

The occurrence of kala-azar in children in the first year of life presents certain unusual advantages for the study of the epidemiology of the disease. In the first place, the simple life of an infant with respect to diet, contact and whereabouts renders many of the possible channeIs. ofinfection in an adult reIatively unimportant in a young child, thus greatly reducing the epidemiologicalfactors to be considered. Secondly, information concerning an infant, generaHy speaking, can be obtained more accurately than in the case of an older child, partly because his. personalhistory is brief and partly because he is usually under the close attention and care of his mother. These are no small advantages in a disease the onset of which is, in most case乳 insidious and the incubation period of which is little known except forits being rather long and variable. Finally,infancy affords a unique opportumty to ascertam whether the transmission of the infection is limited to a certain season, or whether there is, in the year, a period of greatest infectivity. Such a finding, if established, would rute out possibilities of Jittle signi- ficance, and throw new light, on the transmission problem of the disease.     

A gastric duplication cyst at the splenic hilum mimicking endometriosis clinically in a female adult

Gastric duplication is a congenital malformation occurring mostly in infants or childhood. It is rarely found in adults. Some are completely separate cystic lesions unconnected to the stomach, which makes them more difficult to diagnose in a clinical setting. Differential diagnoses of this separate form often include a pancreatic pseudocyst or pancreatic cystic tumor according to the anatomic location. Some associated anomalies have been documented in the literature, but these are rare. Herein, we report a case of gastric duplication at the splenic hilum of a young female adult with a clinical impression of endometriosis due to the coexistence of a fight ovarian cyst and image findings.     

Rare cavernous lymphangioma of the bladder in an adult female：treatment and review of the literature

Objective： Lymphangioma is a benign tumor representing a congenital malformation of the lymphatic channels. The cavernous lymphangioma of the bladder did not report before. Here we report 1 case of cavernous lymphangioma of the bladder in an adult female and review the literature in order to accumulate the experience of diagnosis and treatment for these diseases. Methods： In our case a 50-year-old woman presented with irritative voiding symptoms and had painless macroscopic hematuria at times. Cystoscopy showed a non-papillary tumor at apex vesicae and mucous membrane hyperaemia between the two orifices within the trigone. The pathologic diagnosis was cystitis glandularis with hyperplasia of urothelium and cavernous lymphangioma in lamina propria. Transurethral resection was performed and then bleomycin A5 was injected into lesion multipoint applying ureteral catheter with puncture needle. Results： Two months after operation the irritative voiding symptoms improved and the urine analysis was normal. Cystoscopy showed no residual tumor. Bleomycin A5 was injected into the lesion area again just like the operation before. All symptoms disappeared completely when the patient was examined a month later. There was no side effect after injection and no recurrence during the follow-up of 1 year. Conclusion： Lymphangioma of the bladder can be diagnosed exactly by cystoscopy and pathological examination. Surgery may be the best treatment. The bleomycin A5 intralesional sclerosant is also an effective therapy for the disease after surgical removal.